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在“Elsevier电子期刊”中，命中：142条，耗时：小于0.01 秒

在所有数据库中总计命中：302条

1.Significance of aberrant glial cell phenotypes in pathophysiology of amyotrophic lateral sclerosis

作者：Emiliano Trias ; Sofia Ibarburu ; Romina Barreto-Nú ; ñ ; ez ; Luis Barbeito ; ^{barbeito@pasteur.edu.uy}

关键词：AbAs ; Motor neurons ; ALS ; Neurodegenerative cellular microenvironment

刊名：Neuroscience Letters

出版年：2017

2.Gorham disease: lymphangiomatosis with massive osteolysis

作者：Ryan M. Renacci^a ; ^{rmr92@georgetown.edu} ; Roger J. Bartolotta^b ; ^{rob9074@med.cornell.edu}

关键词：Gorham disease ; Vanishing bone disease ; Lymphangiomatosis ; MRI ; Radiation

刊名：Clinical Imaging

出版年：2017

3.MicroRNAs-424 and 206 are potential prognostic markers in spinal onset amyotrophic lateral sclerosis

作者：Helen M.T. de Andrade^a ; Milena de Albuquerque^a ; Simoni H. Avansini^b ; Cristiane de S. Rocha^b ; Danyella B. Dogini^b ; Anamarli Nucci^a ; Benilton Carvalho^b ; Iscia Lopes-Cendes^b ; Marcondes C. Franç ; a Jr.^a ; ^{mcfrancajr@uol.com.br" class="auth_mail" title="E-mail the corresponding author}

关键词：MicroRNA ; Amyotrophic lateral sclerosis ; Skeletal muscle ; Motor neuron ; Prognosis

刊名：Journal of the Neurological Sciences

出版年：2016

4.Macrophage-mediated inflammation and glial response in the skeletal muscle of a rat model of familial amyotrophic lateral sclerosis (ALS)

作者：Jonathan M. Van Dyke ; Ivy M. Smit-Oistad ; Corey Macrander ; Dan Krakora ; Michael G. Meyer ; Masatoshi Suzuki ; ^{masatoshi.suzuki@wisc.edu" class="auth_mail" title="E-mail the corresponding author}

关键词：α-BTX ; alpha-bungarotoxin ; AChR ; acetylcholine receptor ; ALS ; amyotrophic lateral sclerosis ; ANOVA ; analysis of variance ; BBB ; Basso&ndash ; Beattie&ndash ; Bresnahan hindlimb locomotor rating ; BVC ; bupivacaine hydrochloride ; CD11b ; cluster of differentiation 11b ; CD68 ; cluster of differentiation 68 ; C9ORF72 ; chromosome 9 open reading frame 72 ; EDTA ; Ethylenediaminetetraacetic acid ; EGTA ; ethylene glycol tetraacetic acid ; ELISA ; enzyme-linked immunosorbent assay ; GAPDH ; Glyceraldehyde-3-phosphate de

刊名：Experimental Neurology

出版年：2016

5.Differentiation of control and ALS mutant human iPSCs into functional skeletal muscle cells, a tool for the study of neuromuscolar diseases

作者：Jessica Lenzi^a ; ^b ; Francesca Pagani^a ; Riccardo De Santis^a ; ^b ; Cristina Limatola^c ; Irene Bozzoni^a ; ^b ; ^d ; Silvia Di Angelantonio^a ; ^c ; Alessandro Rosa^b ; ^{alessandro.rosa@uniroma1.it" class="auth_mail" title="E-mail the corresponding author}

关键词：Induced Pluripotent Stem Cells ; Amyotrophic Lateral Sclerosis ; FUS/TLS ; TDP-43 ; Skeletal muscle

刊名：Stem Cell Research

出版年：2016

6.Mitochondrial Lon protease in human disease and aging: Including an etiologic classification of Lon-related diseases and disorders

作者：Daniela A. Bota^a ; ^{dbota@uci.edu" class="auth_mail" title="E-mail the corresponding author} ; Kelvin J.A. Davies^b ; ^c

关键词：ALAS-1 ; 5-Aminolevulinic acid synthase ; ALS ; Amyotrophic Lateral Sclerosis ; CDDO ; 2-cyano-3 ; 12-dioxooleana-1 ; 9-dien-28-oic acid ; CODAS ; Cerebral ; ocular ; Dental ; Auricular ; Skeletal Anomalies Syndrome ; EGF ; Epidermal Growth Factor ; ERK ; Extracellular signal-regulated protein kinase ; ER ; endoplasmic reticulum ; ETC ; electron transport chain ; FRDA ; Friedreich ataxia ; GRP78 ; 78 ; ; kDa glucose-regulated protein ; HAART ; highly active antiretroviral therapy ; HIF-1 ; Hypoxia-inducible factor 1 ; H

刊名：Free Radical Biology and Medicine

出版年：2016

7.Caspase 6 has a protective role in SOD1^G93A transgenic mice

作者：Marion C. Hogg ; Mollie R. Mitchem¹ ; Hans-Georg Kö ; nig ; Jochen H.M. Prehn ; ^{prehn@rcsi.ie" class="auth_mail" title="E-mail the corresponding author}

关键词：AD ; Alzheimer's disease ; ALS ; amyotrophic lateral sclerosis ; Casp6/C6 ; caspase 6 ; NGF ; nerve growth factor ; NMJ ; neuromuscular junction ; Ntg ; non-transgenic ; PND ; post-natal day ; SOD1 ; superoxide dismutase 1 ; STS ; staurosporine ; Tg ; transgenic

刊名：Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

出版年：2016

8.Lack of age-related clinical progression in PGC-1α-deficient mice - implications for mitochondrial encephalopathies

作者：Levente Szalardy^a ; ^{levente.szalardy@yahoo.com" class="auth_mail" title="E-mail the corresponding author} ; Mate Molnar^a ; ^{matem87@gmail.com" class="auth_mail" title="E-mail the corresponding author} ; Rita Torok^a ; ^{torok.rituska@gmail.com" class="auth_mail" title="E-mail the corresponding author} ; Denes Zadori^a ; ^{zadorid@gmail.com" class="auth_mail" title="E-mail the corresponding author} ; Gabor G. Kovacs^b ; ^{gabor.kovacs@meduniwien.ac.at" class="auth_mail" title="E-mail the corresponding author} ; Laszlo Vecsei^a ; ^c ; ^{vecsei.laszlo@med.u-szeged.hu" class="auth_mail" title="E-mail the corresponding author} ; Peter Klivenyi^a ; ^{klivenyi.peter@med.u-szeged.hu" class="auth_mail" title="E-mail the corresponding author}

关键词：AD ; Alzheimer&rsquo ; s disease ; ALS ; amyotrophic lateral sclerosis ; CNS ; central nervous system ; COX ; cythochrome oxidase ; ERR ; estrogen-related receptor ; FL-PGC-1α ; full-length PGC-1α ; GFAP ; glial fibrillary acidic protein ; HE ; hematoxylin and eosin ; HD ; Huntington&rsquo ; s disease ; KLB ; Klü ; ver-Barrera staining ; KSS ; Kearns-Sayre syndrome ; LS ; Leigh syndrome ; MEF2C ; myocyte-specific enhancer factor 2C ; MELAS ; mitochondrial encephalomyopathy ; lactic acidosis and stroke-like episodes ; MERRF ; m

刊名：Behavioural Brain Research

出版年：2016

9.Pyle disease (metaphyseal dysplasia) presenting in two adult sisters

作者：Diego Ximenes Soares ; MD^a ; ^{diegoximenessoares@yahoo.com.br} ; Amá ; lia Mapurunga Almeida ; MD^b ; André ; Rodrigues Faç ; anha Barreto ; MD^a ; Ilze Jucá ; Alencar e Silva ; MD^b ; José ; Daniel Vieira de Castro ; MD ; PhD^c ; Francisco José ; Magalhã ; es Pinto ; MD^a ; Daniel Aguiar Dias ; MD^a ; Lindenberg Barbosa Aguiar ; MD^a

关键词：Pyle's disease ; Metaphyseal dysplasia ; Erlenmeyer flask

刊名：Radiology Case Reports

出版年：2016

10.Cartilage oligomeric matrix protein participates in the pathogenesis of liver fibrosis

作者：Fernando Magdaleno¹ ; ² ; ^&dagger ; ; Elena Arriazu¹ ; ^&dagger ; ; Marina Ruiz de Galarreta¹ ; ^&dagger ; ; Yu Chen² ; Xiaodong Ge¹ ; ² ; Laura Conde de la Rosa¹ ; Natalia Nieto¹ ; ² ; ^{nnieto@uic.edu" class="auth_mail" title="E-mail the corresponding author}

关键词：ALT ; alanine aminotransferase ; AST ; aspartate aminotransferase ; CCl4 ; carbon tetrachloride ; COMP ; cartilage oligomeric matrix protein ; Comp&minus ; /&minus ; cartilage oligomeric matrix protein global knockout mice ; CV ; central vein ; ECM ; extracellular matrix ; GAPDH ; glyceraldehyde-3-phosphate dehydrogenase ; H&E ; hematoxylin and eosin ; HSC(s) ; hepatic stellate cell(s) ; IHC ; immunohistochemistry ; IOD ; integrated optical density ; MMP(s) ; matrix metalloproteinase(s) ; MO ; mineral oil ; rCOMP ; recombina

刊名：Journal of Hepatology

出版年：2016

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