搜索页_+glutaryl-CoA+dehydrogenase+deficient+mice

常用资源

电子图书

期刊论文

学位会议

外文资源

特色专题

内部出版物

SpringerLink电子期刊(4)

Elsevier电子期刊(7)

在“Elsevier电子期刊”中，命中：7条，耗时：0.0709374 秒

在所有数据库中总计命中：11条

1.Experimental evidence that overexpression of NR2B glutamate receptor subunit is associated with brain vacuolation in adult glutaryl-CoA dehydrogenase deficient mice: A potential role for glutamatergic-induced excitotoxicity in GA I neuropathology

作者：Marí ; lia Danyelle Nunes Rodrigues^a ; Bianca Seminotti^a ; Alexandre Umpierrez Amaral^a ; Guilhian Leipnitz^a ; Stephen Irwin Goodman^b ; Michael Woontner^b ; Diogo Onofre Gomes de Souza^a ; Moacir Wajner^a ; ^c ; ^{mwajner@ufrgs.br" class="auth_mail" title="E-mail the corresponding author}

关键词：Glutaric aciduria type I ; Glutamate receptors ; Glutamate transporter ; Excitotoxicity

刊名：Journal of the Neurological Sciences

出版年：2015

2.Neurodevelopmental and cognitive behavior of glutaryl-CoA dehydrogenase deficient knockout mice

作者：Estela Natacha Brandt Busanello^a ; Letí ; cia Pettenuzzo^a ; Paulo Henrique Botton^a ; Pablo Pandolfo^b ; Diogo Onofre Gomes de Souza^a ; Michael Woontner^c ; Stephen Goodman^c ; David Koeller^d ; ^e ; Moacir Wajner^a ; ^f ; ^{mwajner@ufrgs.br}

关键词：Glutaric acidemia type I ; Mice behavior ; Cognitive behavior ; Climbing behavior ; Neurodevelopment ; Knockout mice model

刊名：Life Sciences

出版年：2013

3.Marked reduction of Na⁺, K⁺-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice

作者：Alex ; re Umpierrez Amaral ; Cristiane Cecatto ; Bianca Seminotti ; ?ngela Zanatta ; Carolina Gon?alves Fern ; es ; Estela Natacha Br ; t Busanello ; Luisa Macedo Braga ; C¨¦sar Augusto Jo?o Ribeiro ; Diogo Onofre Gomes de Souza ; Michael Woontner ; David M. Koeller ; Stephen Goodman ; Moacir Wajner

关键词：CK ; creatine kinase ; DCIP ; dichloroindophenol ; EDTA ; ethylenediaminetetracetic acid ; GA ; glutaric acid ; GA I ; glutaric acidemia type I ; GCDH ; glutaryl-CoA dehydrogenase ; Gcdh&minus ; /&minus ; glutaryl-CoA dehydrogenase deficient mice ; 3HGA ; 3-hydroxyglutar

刊名：Molecular Genetics and Metabolism

出版年：2012

4.Disruption of brain redox homeostasis in glutaryl-CoA dehydrogenase deficient mice treated with high dietary lysine supplementation

作者：Bianca Seminotti^a ; Alexandre Umpierrez Amaral^a ; Mateus Struecker da Rosa^a ; Carolina Gonç ; alves Fernandes^a ; Guilhian Leipnitz^a ; Silvia Olivera-Bravo^b ; Luis Barbeito^b ; Cé ; sar Augusto J. Ribeiro^a ; Diogo Onofre Gomes de Souza^a ; Michael Woontner^c ; Stephen I. Goodman^c ; David M. Koeller^d ; Moacir Wajner^a ; ^e ; ^{mwajner@ufrgs.br}

关键词：CAT ; catalase ; DCF-DA ; 2-7-dihydrodichlorofluorescein diacetate ; DCFH ; 2-7-dihydrodichlorofluorescein ; DTNB ; 5-5-dithio-bis (2-nitrobenzoic acid) ; EDTA ; ethylenediamine tetraacetic acid ; GA I ; glutaric aciduria type I ; GA ; glutaric acid ; Gcdh&minus ; /&minu

刊名：Molecular Genetics and Metabolism

出版年：2013

5.Induction of oxidative stress in brain of glutaryl-CoA dehydrogenase deficient mice by acute lysine administration

作者：Bianca Seminotti^a ; Mateus Struecker da Rosa^a ; Carolina Gonç ; alves Fernandes^a ; Alexandre Umpierrez Amaral^a ; Luisa Macedo Braga^b ; Guilhian Leipnitz^a ; Diogo Onofre Gomes de Souza^a ; Michael Woontner^c ; David M. Koeller^d ; ^e ; Stephen Goodman^c ; Moacir Wajner^a ; ^f ; ^{mwajner@ufrgs.br}

刊名：Molecular Genetics and Metabolism

出版年：2012

6.Reduction of Na⁺, K⁺-ATPase activity and expression in cerebral cortex of glutaryl-CoA dehydrogenase deficient mice: A possible mechanism for brain injury in glutaric aciduria type I

作者：Alexandre Umpierrez Amaral^a ; Bianca Seminotti^a ; Cristiane Cecatto^a ; Carolina Gonç ; alves Fernandes^a ; Estela Natacha Brandt Busanello^a ; Â ; ngela Zanatta^a ; Luiza Wilges Kist^b ; Maurí ; cio Reis Bogo^b ; Diogo Onofre Gomes de Souza^a ; Michael Woontner^c ; Stephen Goodman^c ; David M. Koeller^d ; Moacir Wajner^a ; ^e ; ^{mwajner@ufrgs.br}

关键词：CK ; creatine kinase ; DCIP ; dichloroindophenol ; DNP ; dinitrophenol ; EDTA ; ethylenediaminetetracetic acid ; EGTA ; ethylene glycol-bis(2-aminoethylether)-NN ; N&prime ; N&prime ; -tetraacetic acid ; GA ; glutaric acid ; GA I ; glutaric acidemia type I ; GCDH ; glutaryl

刊名：Molecular Genetics and Metabolism

出版年：2012

7.Glutaconyl-CoA is the main toxic agent in glutaryl-CoA dehydrogenase deficiency (glutaric aciduria type I)

作者：Willy Lehnert ; Jö ; rn Oliver Sass

刊名：Medical Hypotheses

出版年：2005

按检索点细分(7)

题名(6)

关键词(1)

文摘(5)

按出版年细分(7)

2015年(1)

2013年(2)

2012年(3)

2005年(1)

地址：北京市海淀区学院路29号邮编：100083

电话：办公室：(+86 10)66554848；文献借阅、咨询服务、科技查新：66554700