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在“Elsevier电子期刊”中，命中：132条，耗时：0.0279782 秒

在所有数据库中总计命中：173条

1.“Role of peroxisomes in human lipid metabolism and its importance for neurological development”

作者：Ronald J.A. Wanders^a ; ; Bwee Tien Poll-The^b ; ^{r.j.wanders@amc.uva.nl}

关键词：Peroxisomes ; Peroxisomal disorders ; Lipidomics ; Lipids ; Fatty acids ; Mitochondria

刊名：Neuroscience Letters

出版年：2017

2.Ginger extract increases muscle mitochondrial biogenesis and serum HDL-cholesterol level in high-fat diet-fed rats

作者：Soojung Oh^a ; ¹ ; Mak-Soon Lee^a ; ¹ ; Sunyoon Jung^a ; ¹ ; Seunghae Kim^a ; Hyeyoung Park^a ; Seonyoung Park^a ; Seog-Young Kim^a ; Chong-Tai Kim^b ; Young-Hee Jo^b ; In-Hwan Kim^c ; Yangha Kim^a ; ^{yhmoon@ewha.ac.kr}

关键词：ABCA1 ; ATP-binding cassette transporter A1 ; ApoA-1 ; apolipoprotein A-1 ; CYP7A1 ; 7 alpha-hydroxylase ; GEH ; high-fat diet containing 0.5% ginger extract ; GEL ; high-fat diet containing 0.25% ginger extract ; HDL-C ; high-density lipoprotein-cholesterol ; HF ; high-fat diet ; LCAT ; lecithin-cholesterol acyltransferase ; LDL-C ; low-density lipoprotein-cholesterol ; mtDNA ; mitochondrial DNA ; NRF ; nuclear respiratory factor ; PGC-1α ; peroxisome proliferator-activated receptor γ coactivator-1α ; PPAR ; peroxisome

刊名：Journal of Functional Foods

出版年：2017

3.Peroxisome biogenesis disorders in the Zellweger spectrum: An overview of current diagnosis, clinical manifestations, and treatment guidelines

作者：Nancy E. Braverman^a ; ^{nancy.braverman@mcgill.ca" class="auth_mail" title="E-mail the corresponding author} ; Gerald V. Raymond^b ; ^{gvraymon@umn.edu" class="auth_mail" title="E-mail the corresponding author} ; William B. Rizzo^c ; ^{wrizzo@umnc.edu" class="auth_mail" title="E-mail the corresponding author} ; Ann B. Moser^d ; ^{mosera@kennedykrieger.org" class="auth_mail" title="E-mail the corresponding author} ; Mark E. Wilkinson^e ; ^{mark-wilkinson@uiowa.edu" class="auth_mail" title="E-mail the corresponding author} ; Edwin M. Stone^e ; ^{edwin-stone@uiowa.edu" class="auth_mail" title="E-mail the corresponding author} ; Steven J. Steinberg^f ; ^{ssteinb8@jhmi.edu" class="auth_mail" title="E-mail the corresponding author} ; Michael F. Wangler^g ; ^{michael.wangler@bcm.edu" class="auth_mail" title="E-mail the corresponding author} ; Eric T. Rush^h ; ^{erush@unmc.edu" class="auth_mail" title="E-mail the corresponding author} ; Joseph G. Haciaⁱ ; ^{hacia@usc.edu" class="auth_mail" title="E-mail the corresponding author} ; Mousumi Bose^j ; ^{mousumi@thegfpd.org" class="auth_mail" title="E-mail the corresponding author}

关键词：AAV ; adeno-associated virus ; AED ; anti-epileptic drug(s) ; DHA ; docosahexaenoic acid ; DHCA ; dihydroxycholestanoic acid ; ERG ; electroretinogram ; G-tube ; gastrostomy tube ; IRD ; infantile Refsum disease ; LC-MS/MS ; liquid chromatography/tandem mass spectrometry ; NALD ; neonatal adrenoleukodystrophy ; OCT ; optical coherence tomography ; PBD ; peroxisome biogenesis disorder ; PBD-ZSD ; peroxisome biogenesis disorder-Zellweger spectrum disorder ; THCA ; trihydroxycholestanoic acid ; VLCFA ; very long chain fatty

刊名：Molecular Genetics and Metabolism

出版年：2016

4.Hepatic dysfunction in peroxisomal disorders

作者：Myriam Baes^a ; ^{myriam.baes@pharm.kuleuven.be" class="auth_mail" title="E-mail the corresponding author} ; Paul P. Van Veldhoven^b ; ^{paul.vanveldhoven@med.kuleuven.be" class="auth_mail" title="E-mail the corresponding author}

关键词：ABC ; ATP-binding cassette ; ACAA1 ; acetyl-CoA acyltransferase ; ACOX ; acyl-CoA oxidase ; BAAT ; bile acid CoA-amino acid N-acyl transferase ; C24-bile acid ; cholanoic acid ; C27-bile acid ; cholestanoic acid ; CDCA ; chenodeoxycholic acid ; Cn-DCA ; straight chain dicarboxylic acid with n C atoms ; DCA ; dicarboxylic acid ; DHA ; docosahexaenoic acid ; DHCA ; dihydroxycholestanoic acid ; HAO ; 2-hydroxy acid oxidase ; ER ; endoplasmic reticulum ; MFP ; multifunctional protein ; PBD ; peroxisome biogenesis disorder ; PMP

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

5.De novo peroxisome biogenesis: Evolving concepts and conundrums

作者：Gaurav Agrawal ; Suresh Subramani ; ^{ssubramani@ucsd.edu" class="auth_mail" title="E-mail the corresponding author}

关键词：aa ; amino acids ; ARF1 ; ADP-ribosylation-factor 1 ; APX ; ascorbate peroxidase ; BFA ; brefeldin A ; BY-2 ; bright yellow-2 ; COP ; coatomer protein ; ER ; endoplasmic reticulum ; ERES ; endoplasmic reticulum exit sites ; ERPIC ; ER-peroxisome intermediate compartment ; ERGIC ; ER-Golgi intermediate compartment ; GFP ; green fluorescent protein ; HA ; hemagglutinin ; p33 ; 33-kDa replication protein ; Pex ; peroxin ; PBD ; peroxisome biogenesis disorder ; PMP ; Peroxisomal membrane protein ; pER ; pre-peroxisomal ER ; pMVBs ; p

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

6.Peroxisome biogenesis in mammalian cells: The impact of genes and environment

作者：Rebecca L. Farr^a ; ^b ; Celien Lismont^a ; Stanley R. Terlecky^b ; Marc Fransen^a ; ^{marc.fransen@med.kuleuven.be" class="auth_mail" title="E-mail the corresponding author}

关键词：Age-related disease ; Biogenesis disorder ; Epigenetics ; Intracellular signaling ; Mitochondria ; Peroxisome

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

7.Human disorders of peroxisome metabolism and biogenesis

作者：Hans R. Waterham ; ^{h.r.waterham@amc.uva.nl" class="auth_mail" title="E-mail the corresponding author} ; Sacha Ferdinandusse ; Ronald J.A. Wanders

关键词：ACAA1 ; 3-ketoacyl-CoA thiolase ; ACOX1 ; Acyl-CoA oxidase 1 ; ACOX2 ; acyl-CoA oxidase 2 ; ABCD1 ; ABC transporter D1 ; ABCD2 ; ABC transporter D2 ; ABCD3 ; ABC transporter D3 ; AGPS ; alkyl-dihydroxyacetonephosphate synthase ; AGT ; alanine-glyoxylate aminotransferase ; AMACR ; 2-methylacyl-CoA racemace ; BAAT ; Bile acid&ndash ; CoA ; amino acid N-acyltransferase ; brAcyl ; branched-acyl ; CA ; cholic acid ; CAT ; catalase ; CDCA ; chenodeoxycholic acid ; CoA ; coenzyme A ; DBP ; D-bifunctional protein ; DCA ; dicarboxylic acids

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

8.Multiple paths to peroxisomes: Mechanism of peroxisome maintenance in mammals

作者：Rong Hua ; Peter K. Kim ; ^{pkim@sickkids.ca" class="auth_mail" title="E-mail the corresponding author}

关键词：CHO ; Chinese hamster ovary ; DLP1 ; dynamin-like protein 1 ; ER ; endoplasmic reticulum ; FIS1 ; fission 1 ; H. polymorpha ; Hansenula polymorpha ; MFF ; mitochondrial fission factor ; MAPL ; mitochondria-anchored protein ligase ; MDV ; mitochondria-derived vesicle ; mPTS ; integral membrane targeting sequence ; PAGFP ; photo-activable GFP ; PBD ; peroxisomal biogenesis disorders ; PMP ; peroxisomal membrane protein ; PPAR ; peroxisome-proliferator-activated receptors ; PTS ; peroxisomal targeting signals ; S. cerevisiae

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

9.Proliferation and fission of peroxisomes ‿An update

作者：Michael Schrader^a ; ^b ; ^{m.schrader@exeter.ac.uk" class="auth_mail" title="E-mail the corresponding author} ; Joseph L. Costello^a ; Luis F. Godinho^b ; Afsoon S. Azadi^a ; Markus Islinger^c

关键词：ER ; endoplasmic reticulum ; GC ; glucocorticoid ; GREs ; glucocorticoid response element ; GR ; glucocorticoid receptor ; mTOR ; mammalian target of rapamycin ; ORE ; oleate response elements ; PBD ; peroxisome biogenesis disorder ; PEX ; peroxin ; PPAR ; peroxisome proliferator-activated receptor ; PPRE ; peroxisome proliferator response element ; PTS ; peroxisomal targeting signal ; ROS ; reactive oxygen species

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

10.Targeting and insertion of peroxisomal membrane proteins: ER trafficking versus direct delivery to peroxisomes

作者：Peter U. Mayerhofer ^{mayerhofer@em.uni-frankfurt.de" class="auth_mail" title="E-mail the corresponding author}

关键词：APX ; Ascorbate peroxidase ; ER ; Endoplasmic reticulum ; Get ; Guided entry of TA proteins ; PBD ; Peroxisomal biogenesis disorder ; PMPs ; Peroxisomal membrane proteins ; PTS ; Peroxisomal targeting signals ; RNC ; Ribosome nascent chain complex ; SRP ; Signal recognition particle ; TA ; Tail-anchored ; TMS ; Transmembrane segments ; ZS ; Zellweger syndrome

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

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