Sudden cardiac death in neuromuscular disorders
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文摘

Patients with certain neuromuscular disorders carry an increased risk to experience sudden cardiac death

Risk of SCD is particularly increased in myotonic dystrophy, mitochondrial disorders, laminopathies, and desminopathies.

Risk factors to develop sudden cardiac death vary considerably between neuromuscular disorders.

Risk factors for SCD include fibrosis, QT-prolongation, increased QT-dispersion, early repolarization, or T-wave alternans.

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