Patients with certain neuromuscular disorders carry an increased risk to experience sudden cardiac death
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Risk of SCD is particularly increased in myotonic dystrophy, mitochondrial disorders, laminopathies, and desminopathies.
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Risk factors to develop sudden cardiac death vary considerably between neuromuscular disorders.
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Risk factors for SCD include fibrosis, QT-prolongation, increased QT-dispersion, early repolarization, or T-wave alternans.
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