Life-threatening anomalies of the thoracic duct: Anatomic delineation dictates management

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• 作者：Steven J. Fishman ; Patricia E. Burrows ; Joseph Upton ; W. Hardy Hendren
• 关键词：Hemangioma ; diaphragm ; hydrops fetalis ; newborn
• 刊名：Journal of Pediatric Surgery
• 出版年：2001
• 出版时间：August 2001
• 年：2001
• 卷：36
• 期：8
• 页码：1269-1272
• 全文大小：189 K

文摘

Congenital anomalies of the thoracic duct are rare, poorly characterized, and difficult to manage. The spectrum of pathophysiologic perturbations, presenting symptoms, radiographic findings, and interventions performed in 4 patients are shown. Accurate anatomic delineation of the malformation was only possible by direct injection contrast lymphangiography. Therapies tailored to address the anatomic aberrations included intralesional sclerotherapy, surgical excision and ligation, lymphovenous anastomosis, and omental interposition to interrupt dysfunctional collateral lymphatics to the lung. Accurate anatomic diagnosis of central lymphatic channel anomalies by contrast lymphangiography facilitates an individualized multidisciplinary approach to repair. J Pediatr Surg 36:1269-1272.