Hepatoblastoma is the most common primary liver tumor for children under 5 years of age, with an incidence of 5.2 per million.

Diagnosis depends on imaging studies, AFP levels and percutaneous biopsy.

Treatment modality is usually surgical with neoadjuvant chemotherapy.

Remission and long term survival can be achieved after complete anatomical resection and appropriate neoadjuvant chemotherapy.

Hepatoblastoma cases should be referred to specialized centers for management.