Cor Triatriatum Sinister diagnosed in adult life with three dimensional transesophageal echocardiography
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  • 作者:Righab Hamdan (1)
    Nicolas Mirochnik (2)
    David Celermajer (3)
    Pierre Nassar (2)
    Laurence Iserin (2)
  • 刊名:BMC Cardiovascular Disorders
  • 出版年:2010
  • 出版时间:December 2010
  • 年:2010
  • 卷:10
  • 期:1
  • 全文大小:601KB
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    2. Bassareo PP, Tumbarello R, Mercuro G: <strong class="a-plus-plus">Cor triatriatum and lipomatous hypertrophy of the interatrial septum in the elderly: a case report.strong> / Cardiovasc Ultrasound 2010, <strong class="a-plus-plus">9:strong>8鈥?.
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    11. The pre-publication history for this paper can be accessed here:ss="a-plus-plus">http://www.biomedcentral.com/1471-2261/10/54/prepub
  • 作者单位:Righab Hamdan (1)
    Nicolas Mirochnik (2)
    David Celermajer (3)
    Pierre Nassar (2)
    Laurence Iserin (2)

    1. Saint Antoine Hospital, Paris, France
    2. European hospital Georges Pompidou, Paris, France
    3. Scandrett Professor of Cardiology, University of Sydney Clinical Academic Cardiologist, Royal Prince Alfred Hospital, Sydney, Australia
文摘
Background Cor triatriatum is a very rare congenital abnormality, usually symptomatic during childhood, diagnosis in adult age is less common. Case Presentation We report the case of a 40 years old woman referred to our hospital for atrial flutter ablation, transthoracic cardiac bidimensional echocardiography showed an abnormal membrane bisecting the left atrium, the diagnosis of cor triatriatum was fully made via three dimensional transesophageal echocardiography. More interstingly three other cardiac anomalies were associated: ostium secundum atrial septal defect, dilated coronary sinus due probably to persistent left superior vena cava and normally functioning bicuspid aortic valve. Conclusions Cor triatriatum sinister in adult life is important to recognize because it may be easily surgically correctable when hemodynamically significant. Three Dimensional transesophageal echocardiography is a minimally invasive and highly sensitive diagnostic modality.
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