Endovascular treatment of genetically linked aortic diseases

详细信息    查看全文

• 作者：Prof. Dr. D. Böckler ; K. Meisenbacher ; A. S. Peters ; C. Grond-Ginsbach…
• 关键词：Connective tissue disease ; Marfan ; Aorta ; Endovascular aortic repair ; Thoracic endovascular aortic repair
• 刊名：Gefässchirurgie
• 出版年：2017
• 出版时间：March 2017
• 年：2017
• 卷：22
• 期：1-supp
• 页码：1-7
• 全文大小：532KB
• 刊物主题：Vascular Surgery;
• 出版者：Springer Medizin
• ISSN：1434-3932
• 卷排序：22

文摘

BackgroundThe most important structural proteins of the vascular wall are collagen and elastin. Genetically linked connective tissue diseases lead to degeneration, aneurysm formation and spontaneous dissection or rupture of arteries. The most well-known are Marfan syndrome, vascular Ehlers-Danlos syndrome (type IV), Loeys-Dietz syndrome and familial aortic aneurysms and dissections.