Orthotropic heart transplantation for adult congenital heart disease: a case with heterotaxy and dextrocardia

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• 作者：Hikaru Matsuda ; Norihide Fukushima…
• 关键词：Adult congenital heart disease ; Heart transplantation ; Heterotaxy ; Dextrocardia ; Humoral rejection
• 刊名：General Thoracic and Cardiovascular Surgery
• 出版年：2017
• 出版时间：January 2017
• 年：2017
• 卷：65
• 期：1
• 页码：47-51
• 全文大小：
• 刊物主题：Thoracic Surgery; Cardiac Surgery; Cardiology; Surgical Oncology;
• 出版者：Springer Japan
• ISSN：1863-6713
• 卷排序：65

文摘

A 41-year-old male with heterotaxy (left isomerism) and dextrocardia composed by single ventricle, absent inferior vena cava, bilateral superior vena cava (SVC), common atrioventricular valve has received orthotopic heart transplantation (HTx) after long waiting period as Status-1. Reconstructions of bilateral SVC and hepatic vein route were successful without use of prosthetic material, and the donor heart was placed in the left mediastinum. In spite of satisfactory early recovery, the patient expired 4 months after transplantation mainly from fungal infection which developed following humoral rejection. HTx for adult patients with complex congenital heart disease is demanding in technical as well as pre- and post-transplant management, and indication should be critically determined.