Heterotaxy and intestinal rotation anomalies: 20?years experience at a UK regional paediatric surgery centre

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• 作者：Paul S. Cullis ; Sotirios Siminas ; Adeline Salim…
• 关键词：Heterotaxy ; Intestinal rotation ; Cardiac anomalies ; Ladd’s operation ; Outcomes
• 刊名：Pediatric Surgery International
• 出版年：2015
• 出版时间：December 2015
• 年：2015
• 卷：31
• 期：12
• 页码：1127-1131
• 全文大小：483 KB
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• 作者单位：Paul S. Cullis (1)
  Sotirios Siminas (2)
  Adeline Salim (3)
  Robert Johnson (4)
  Paul D. Losty (3) (5)
  
  1. Department of Surgical Paediatrics, The Royal Hospital for Sick Children, Yorkhill, Glasgow, UK
  2. Department of Paediatric Surgery, Royal Manchester Children’s Hospital, Manchester, UK
  3. Department of Paediatric Surgery, Alder Hey Childrens Hospital NHS Foundation Trust, Liverpool, UK
  4. Department of Paediatric Cardiology, Alder Hey Childrens Hospital NHS Foundation Trust, Liverpool, UK
  5. Institute of Child Health, University of Liverpool, Liverpool, UK
  
• 刊物类别：Medicine
• 刊物主题：Medicine & Public Health
  Pediatrics
  Surgery
  Pediatric Surgery
  
• 出版者：Springer Berlin / Heidelberg
• ISSN：1437-9813

文摘

Background The association of heterotaxy with intestinal rotation anomalies is well described. However debate exists with regard optimal management notably should ‘asymptomatic-bowel rotation anomalies undergo operation? The present study therefore sought to determine: (1) the risk(s) of volvulus in patients diagnosed with heterotaxy and (2) define morbidity associated with operation for ‘asymptomatic-anomalies in a fragile patient cohort with co-existent congenital heart disease.