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中国地质文献-英文(4)
SpringerLink电子期刊(1886)
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Elsevier电子期刊(6504)
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NATURE电子期刊(62)
ACS电子期刊(516)
在“
Elsevier电子期刊
”中,
命中:
6,504
条,耗时:小于0.01 秒
在所有数据库中总计命中:
9,048
条
1.
Numerical analysis of the melt behavior in a fuel support piece of the BWR by
MPS
作者:
Ronghua Chen
a
;
Lie Chen
a
;
Kailun Guo
a
;
Akifumi Yamaji
b
;
Masahiro Furuya
c
;
Wenxi Tian
a
;
G.H. Su
a
;
ghsu@mail.xjtu.edu.cn
;
Suizheng Qiu
a
关键词:
MPS
method
;
Fuel support piece
;
Severe accident
;
Freezing behavior
刊名:Annals of Nuclear Energy
出版年:2017
2.
Multi-level energy/power-aware design methodology for
MPS
oC
作者:
Bassem Ouni
a
;
Bassem.Ouni@unice.fr
Author Vitae
;
Imen Mhedbi
b
;
Imen.Mhedhbi@lip6.fr
Author Vitae
;
Chiraz Trabelsi
c
;
chiraz.trabelsi@esiea.fr
Author Vitae
;
Rabie Ben Atitallah
d
;
Rabie.BenAtitallah@univ-valenciennes.fr
Author Vitae
;
Cé
;
cile Belleudy
a
;
Cecile.Belleudy@unice.fr
Author Vitae
关键词:
Power modeling
;
MPS
oC
;
DVFS
;
Design space exploration
;
Transactional level
;
Functional level
刊名:Journal of Parallel and Distributed Computing
出版年:2017
3.
Improved acid recovery performance by novel Poly(DMAEM-co-γ-
MPS
) anion exchange membrane via diffusion dialysis
作者:
Abhishek N. Mondal
;
Congliang Cheng
;
Muhammad Imran Khan
;
Md. Masem Hossain
;
Kamana Emmanuel
;
Liang Ge
;
Bin Wu
;
Yubin He
;
Jin Ran
;
Xiaolin Ge
;
Noor Ul Afsar
;
Liang Wu
;
Tongwen Xu
;
twxu@ustc.edu.cn
关键词:
Anion exchange membrane
;
Diffusion dialysis
;
Acid recovery
;
Separation Performance
;
DMAEM
;
γ-
MPS
刊名:Journal of Membrane Science
出版年:2017
4.
Four novel mutations in the N-acetylgalactosamine-6-sulfate sulfatase gene among Egyptian patients with Morquio A disease
作者:
Ekram M. Fateen
a
;
efateen@yahoo.com
(Professor)
;
Hanan Abd El Mawgoud
b
;
hananmoawad@gmail.com
(Assistant Professor)
;
Noura R. Eissa
c
;
nr.eissa@yahoo.com
(Assistant Reseacher)
;
Mona M. Ibrahim
a
;
monamahmoud60@yahoo.com
(Assistant Professor)
;
Mona S. Aglan
d
;
drmona_aglan@yahoo.com
(Professor)
;
Mona L. Essawi
c
;
mlessawi@yahoo.com
(Professor)
关键词:
MPS
IVA
;
Mucopolysaccharidosis type 4 &ndash
A ;
GALNS
;
N-acetylgalactosamine-6-sulfatase
;
GAGs
;
Glycosaminoglycans
;
NRC
;
National Research Centre
;
MPS
s
;
Mucopolysaccharidoses
;
GLB1
;
β-Galactosidase
;
KS
;
Keratan Sulfate
;
C6S
;
Chondroitin-6-Sulfate
;
kDa
;
Kilo Dalton
;
HGMD
;
Human Gene Mutation Database
;
ERT
;
Enzyme Replacement Therapy
;
LMSDC
;
Limb Malformation and Skeletal Deformities Clinic
;
RFLP
;
Restriction Fragment Length Polymorphism
;
PCR
;
Polymerase Chain Reaction
;
mRNA
;
messenger Ribonucleic
刊名:Gene
出版年:2017
5.
Mucopolysaccharidosis IVA and glycosaminoglycans
作者:
Shaukat Khan
a
;
1
;
Carlos J. Almé
;
ciga-Dí
;
az
b
;
1
;
Kazuki Sawamoto
a
;
William G. Mackenzie
a
;
Mary C. Theroux
a
;
Christian Pizarro
a
;
Robert W. Mason
a
;
Tadao Orii
c
;
Shunji Tomatsu
a
;
c
;
d
;
stomatsu@nemours.org
;
stomatsu@gifu-u.ac.jp
关键词:
MPS
;
mucopolysaccharidosis
;
GAG
;
glycosaminoglycans
;
C6S
;
chondroitin-6-sulfate
;
KS
;
keratin sulfate
;
ECM
;
extracellular matrix
;
GALNS
;
N-acetylgalactosamine 6-sulfate sulfatase
;
LC-MS/MS
;
liquid chromatography/tandem mass spectrometry
;
LSD
;
lysosomal storage disorder
;
DBS
;
dried blood spot
;
DMB
;
dimethylmethylene blue
;
ERT
;
enzyme replacement therapy
;
6MWT
;
6
;
min walk test
;
3
MSCT
;
3
;
min stair climb test
;
ADL
;
activity of daily living
;
HSCT
;
Hematopoietic Stem Cell Therapy
;
BMT
;
bone m
刊名:Molecular Genetics and Metabolism
出版年:2017
6.
Quinidine therapy for West syndrome with KCNTI mutation: A case report
作者:
Masataka Fukuoka
a
;
Ichiro Kuki
a
;
i-kuki@med.osakacity-hp.or.jp
;
Hisashi Kawawaki
a
;
Shin Okazaki
a
;
Kiyohiro Kim
a
;
Yuka Hattori
a
;
Hitomi Tsuji
a
;
Megumi Nukui
a
;
Takeshi Inoue
a
;
Yoko Yoshida
b
;
Takehiro Uda
c
;
Sadami Kimura
d
;
Yukiko Mogami
d
;
Yasuhiro Suzuki
d
;
Nobuhiko Okamoto
e
;
Hirotomo Saitsu
f
;
g
;
Naomichi Matsumoto
f
关键词:
EOEE
;
early onset epileptic encephalopathy
;
MPS
I
;
migrating partial seizures of infancy
;
LTG
;
lamotrigine
;
VPA
;
valproate
刊名:Brain and Development
出版年:2017
7.
Generation of a Spindle Checkpoint Arrest from Synthetic Signaling Assemblies
作者:
Ivan Yuan
1
;
2
;
Ioanna Leontiou
1
;
2
;
Priya Amin
1
;
Karen M. May
1
;
Sadhbh Soper Ní
;
Chafraidh
1
;
Eli&scaron
;
ka Zlá
;
malová
;
1
;
Kevin G. Hardwick
1
;
3
;
kevin.hardwick@ed.ac.uk
关键词:
checkpoint
;
spindle
;
mitosis
;
kinetochore
;
Mad
;
Bub
;
Mps
1
;
synthetic
;
cell cycle
刊名:Current Biology
出版年:2017
8.
Screening for mucopolysaccharidoses in the Turkish population: Analytical and clinical performance of an age-range specific, dye-based, urinary glycosaminoglycan assay
作者:
Khaled El Moustafa
;
MD
a
;
Serap Sivri
;
MD
b
(Professor)
;
Sevilay Karahan
;
PhD
c
;
Turgay Coşkun
;
MD
b
(Professor)
;
Filiz Akbıyık
;
MD
;
PhD
a
(Professor)
;
İncilay Lay
;
MD
;
PhD
a
;
d
;
lincilay@gmail.com
;
isinici@hacettepe.edu.tr
(Associate Prof.)
关键词:
Mucopolysaccharidoses
;
Screening
MPS
s
;
Urinary glycosaminoglycan assay
;
1
;
9-Dimethylene blue
;
Validation
;
Reference intervals
刊名:Clinica Chimica Acta
出版年:2017
9.
Developmental validation of a custom panel including 27
3
SNPs for forensic application using Ion Torrent PGM
作者:
Suhua Zhang
a
;
Yingnan Bian
a
;
Anqi Chen
b
;
Hancheng Zheng
c
;
Yuzhen Gao
c
;
Yiping Hou
d
;
Chengtao Li
a
;
lichengtaohla@16
3
.com
关键词:
Forensic Genetics
;
Personal Genome Machine (PGM)
;
Massively Parallel Sequencing (
MPS
)
;
SNP
刊名:Forensic Science International: Genetics
出版年:2017
10.
MPS
I and carpal tunnel syndrome: analysis using the MPS I Registry
作者:
Nathalie Guffon
a
;
David Viskochil
b
;
Douglas T. Hutchinson
b
;
Christophe Garin
c
;
Kristin A. Moy
d
;
M. Veronica Munoz-Rojas
d
;
Joseph Muenzer
e
刊名:Molecular Genetics and Metabolism
出版年:2017
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作者(1481)
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