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内部出版物
SpringerLink电子期刊(7)
Elsevier电子期刊(9)
在“
Elsevier电子期刊
”中,
命中:
9
条,耗时:0.0119931 秒
在所有数据库中总计命中:
16
条
1.
Disruption of oxidative phosphorylation and synaptic Na
+
, K
+
-ATPase activity by pristanic acid in cerebellum of young rats
作者:
Estela
Natacha
Br
;
t Busanello
;
Vannessa Gon莽alves Araujo Lobato
;
脗ngela Zanatta
;
Carolina Maso Viegas
;
C茅sar Augusto Jo茫o Ribeiro
;
Moacir Wajner
关键词:
Pristanic acid
;
Energy metabolism
;
Peroxisomal biogenesis disorders
;
Rat cerebellum
;
Zellweger syndrome
刊名:Life Sciences
出版年:14 January, 2014
2.
Disturbance of redox homeostasis by ornithine and homocitrulline in rat cerebellum: A possible mechanism of cerebellar dysfunction in HHH syndrome
作者:
?ngela Zanatta
;
Carolina Maso Viegas
;
Anelise Miotti Tonin
;
Estela
Natacha
Br
;
t Busanello
;
Mateus Grings
;
Alana Pimentel Moura
;
Guilhian Leipnitz
;
Moacir Wajner
关键词:
Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome
;
Ornithine
;
Homocitrulline
;
Oxidative stress
;
Cerebellum
刊名:Life Sciences
出版年:2013
3.
Marked reduction of Na
+
, K
+
-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice
作者:
Alex
;
re Umpierrez Amaral
;
Cristiane Cecatto
;
Bianca Seminotti
;
?ngela Zanatta
;
Carolina Gon?alves Fern
;
es
;
Estela
Natacha
Br
;
t Busanello
;
Luisa Macedo
Br
aga
;
C¨¦sar Augusto Jo?o Ribeiro
;
Diogo Onofre Gomes de Souza
;
Michael Woontner
;
David M. Koeller
;
Stephen Goodman
;
Moacir Wajner
关键词:
CK
;
creatine kinase
;
DCIP
;
dichloroindophenol
;
EDTA
;
ethylenediaminetetracetic acid
;
GA
;
glutaric acid
;
GA I
;
glutaric acidemia type I
;
GCDH
;
glutaryl-CoA dehydrogenase
;
Gcdh&minus
;
/&minus
;
glutaryl-CoA dehydrogenase deficient mice
;
3HGA
;
3-hydroxyglutar
刊名:Molecular Genetics and Metabolism
出版年:2012
4.
Neurochemical evidence that glycine induces bioenergetical dysfunction
作者:
Estela
Natacha
Br
;
t Busanello
;
Alana Pimentel Moura
;
Carolina Maso Viegas
;
Â
;
ngela Zanatta
;
Gustavo da Costa Ferreira
;
Patrí
;
cia Fern
;
a Schuck
;
Moacir Wajner
关键词:
Glycine
;
Energy metabolism
;
Rat
;
Br
ain
刊名:Neurochemistry International
出版年:2010
5.
In vitro evidence that phytanic acid compromises Na
+
,K
+
-ATPase activity and the electron flow through the respiratory chain in
br
ain cortex from young rats
作者:
Estela
Natacha
Br
;
t Busanello
;
Carolina Maso Viegas
;
Alana Pimentel Moura
;
Anelise Miotti Tonin
;
Mateus Grings
;
Carmen R. Vargas
;
Moacir Wajner
关键词:
Phytanic acid
;
Peroxisomal disorders
;
Energy metabolism
;
Neurotransmission
刊名:
Br
ain Research
出版年:2010
6.
Selective screening for organic acidemias by urine organic acid GC–MS analysis in
Br
azil: Fifteen-year experience
作者:
Moacir Wajner
;
Daniella de Moura Coelho
;
Rafaela Ingrassia
;
Anderson Bü
;
ker de Oliveira
;
Estela
Natacha
Br
;
t Busanello
;
Kimiyo Raymond
;
Ricardo Flores Pires
;
Carolina Fischinger Moura de Souza
;
Ro
关键词:
Organic acidemias
;
Organic acidurias
;
Organic acids
;
Inborn errors of metabolism
刊名:Clinica Chimica Acta
出版年:2009
7.
In vitro evidence that
d
作者:
Â
;
ngela Zanatta
;
Patrí
;
cia Fern
;
a Schuck
;
Carolina Maso Viegas
;
Lisiane Auré
;
lio Knebel
;
Estela
Natacha
Br
;
t Busanello
;
Alana Pimentel Moura
;
Moacir Wajner
关键词:
d
-Serine
;
Energy metabolism
;
Neurodegeneration
;
Cere
br
al cortex
刊名:
Br
ain Research
出版年:2009
8.
Chronic early postnatal administration of ethylmalonic acid to rats causes behavioral deficit
作者:
Patrí
;
cia Fern
;
a Schuck
;
Gustavo da Costa Ferreira
;
Carolina Maso Viegas
;
Anelise Miotti Tonin
;
Estela
Natacha
Br
;
t Busanello
;
Leticia Ferreira Pettenuzzo
;
Carlos Alex
;
re Netto
;
Moacir Wajner
关键词:
Ethylmalonic acid
;
Water maze
;
Elevated plus maze
;
SCAD deficiency
;
Ethylmalonic aciduria
;
Rat
刊名:Behavioural
Br
ain Research
出版年:2009
9.
Evidence that the major metabolites accumulating in medium-chain acyl-CoA dehydrogenase deficiency disturb mitochondrial energy homeostasis in rat
br
ain
作者:
Patrí
;
cia Fern
;
a Schuck
;
Gustavo da Costa Ferreira
;
Anelise Miotti Tonin
;
Carolina Maso Viegas
;
Estela
Natacha
Br
;
t Busanello
;
Alana Pimentel Moura
;
Â
;
ngela Zanatta
;
Fá
;
bio Klamt
;
Moacir W
关键词:
MCAD deficiency
;
Octanoic acid
;
Decanoic acid
;
Mitochondrial function
;
Rat
br
ain
刊名:
Br
ain Research
出版年:2009
1
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作者(9)
按出版年细分(9)
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2012年(1)
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2009年(4)
2000年及以前(1)
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