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Elsevier电子期刊(26)

在“Elsevier电子期刊”中，命中：26条，耗时：0.010995 秒

在所有数据库中总计命中：26条

1.Very Early Treatment for Infantile-Onset Pompe Disease Contributes to Better Outcomes

作者：Chia-Feng Yang ; MD¹ ; ² ; Chen Chang Yang ; PhD² ; ³ ; Hsuan-Chieh Liao ; MSc⁴ ; ⁵ ; Ling-Yi Huang ; RN⁶ ; Chuan-Chi Chiang ; PhD⁴ ; Hui-Chen Ho ; BS⁷ ; Chih-Jou Lai ; MD⁸ ; Tzu-Hung Chu ; MD¹ ; Tsui-Feng Yang ; MD⁸ ; Ting-Rong Hsu ; MD¹ ; Wen-Jue Soong ; PhD¹ ; Dau-Ming Niu ; MD¹ ; ⁹ ; ^{dmniu1111@yahoo.com.tw" class="auth_mail" title="E-mail the corresponding author}

关键词：AST ; Aspartate aminotransferase ; Bayley-III ; Bayley Scale of Infant and Toddler Development ; Third Edition ; CK ; Creatine kinase ; CRIM ; Cross-reactive immunologic ; ERT ; Enzyme-replacement therapy ; GAA ; Acid α-glucosidase ; IOPD ; Infantile-onset Pompe disease ; LDH ; Lactate dehydrogenase ; LVMI ; Left ventricular mass index ; PDMS-II ; Peabody Development Motor Scale ; Second Edition ; TVGH ; Taipei Veterans General Hospital

刊名：The Journal of Pediatrics

出版年：2016

2.The influence of a polymorphism in the gene encoding angiotensin converting enzyme (ACE) on treatment outcomes in late-onset Pompe patients receiving alglucosidase alfa

作者：Rena C. Baek ; Rachel Palmer ; Robert J. Pomponio ; Yuefeng Lu ; Xiwen Ma ; Alison J. McVie-Wylie ; ^{alison.mcvie-wylie@genzyme.com" class="auth_mail" title="E-mail the corresponding author}

关键词：6MWT ; 6-Minute Walk Test ; ACE ; angiotensin-converting enzyme ; D ; deletion ; ERT ; enzyme replacement therapy ; FVC ; forced vital capacity ; GAA ; acid-alpha glucosidase ; I ; insertion ; IOPD ; infantile-onset Pompe disease ; LOPD ; late-onset Pompe disease ; LOTS ; Late-Onset Treatment Study ; MRI ; magnetic resonance imaging ; PCR ; polymerase chain reaction ; QMT ; quantitative muscle testing

刊名：Molecular Genetics and Metabolism Reports

出版年：2016

3.Divergent clinical outcomes of alpha-glucosidase enzyme replacement therapy in two siblings with infantile-onset Pompe disease treated in the symptomatic or pre-symptomatic state

作者：Takashi Matsuoka^a ; Yoshiyuki Miwa^a ; Makiko Tajika^a ; Madoka Sawada^a ; Koichiro Fujimaki^a ; Takashi Soga^a ; Hideshi Tomita^b ; Shigeru Uemura^b ; Ichizo Nishino^c ; Tokiko Fukuda^d ; Hideo Sugie^e ; Motomichi Kosuga^f ; ^{kosuga-mo@ncchd.go.jp} ; Torayuki Okuyama^g ; Yoh Umeda^a

刊名：Molecular Genetics and Metabolism Reports

出版年：2016

4.GA based decomposition of large scale distributed model predictive control systems

作者：Lei Xie^a ; Xing Cai^b ; Junghui Chen^c ; ^{jason@wavenet.cycu.edu.tw" class="auth_mail" title="E-mail the corresponding author} ; Hongye Su^a

关键词：Distributed model predictive control ; Genetic algorithm ; Input clustering decomposition ; Input&ndash ; output pairing decomposition ; System decomposition

刊名：Control Engineering Practice

出版年：2016

5.Combined aerobic exercise and enzyme replacement therapy rejuvenates the mitochondrial-lysosomal axis and alleviates autophagic blockage in Pompe disease

作者：M.I. Nilsson^a ; L.G. MacNeil^a ; Y. Kitaoka^a ; R. Suri^a ; S.P. Young^b ; J.J. Kaczor^c ; N.J. Nates^a ; M.U. Ansari^a ; T. Wong^a ; M. Ahktar^a ; L. Brandt^a ; B.P. Hettinga^a ; M.A. Tarnopolsky^a ; ^{tarnopol@mcmaster.ca" class="auth_mail" title="E-mail the corresponding author}

关键词：A ; adult ; AET ; aerobic exercise training ; AUC ; area under the curve ; CI-MPR ; cation-independent mannose-6-phosphate receptor ; CLEAR ; coordinated lysosomal expression and regulation transcriptome ; ERT ; enzyme replacement therapy ; FA ; fatty acid ; FG ; fast-twitch glycolytic muscle fibers ; FOG ; fast-twitch oxidative/glycolytic muscle fibers ; GAA ; acid 伪-glucosidase ; GSD II ; glycogen storage disease type II ; I ; infantile ; IOPD ; infantile-onset Pompe disease ; LOPD ; late-onset Pompe disease ; LSD ; lysos

刊名：Free Radical Biology and Medicine

出版年：2015

6.A new assay for fast, reliable CRIM status determination in infantile-onset Pompe disease

作者：Zhaohui Wang ; Patricia Okamoto ; Joan Keutzer

关键词：IOPD ; infantile-onset Pompe disease ; GAA ; acid 伪-glucosidase ; ERT ; enzyme replacement therapy ; rhGAA ; recombinant human GAA ; CRIM ; cross-reactive immunologic material ; ITI ; immune tolerance induction ; PBMC ; peripheral blood mononuclear cell ; PBS ; phosphate-buffered saline ; ACD ; citrate dextrose-A ; EDTA ; ethylenediaminetetraacetic acid ; BSA ; bovine serum albumin ; OD ; optical density ; LDS ; lithium dodecyl sulfate ; DTT ; dithiothreitol ; SDS ; sodium dodecyl sulfate ; PVDF ; polyvinylidene difluoride

刊名：Molecular Genetics and Metabolism

出版年：February, 2014

7.Synthesis and structural characterization of a few thiocarboxylatonickel(II) complexes

作者：Deepak Kumar Joshi ; Subrato Bhattacharya

关键词：Nickel(II) ; Thiocarboxylate ; Metal&ndash ; metal bonding ; Density functional theory ; Magnetism

刊名：Inorganica Chimica Acta

出版年：24 February, 2014

8.Pompe Disease: Early Diagnosis and Early Treatment Make a Difference

作者：Yin-Hsiu Chien ; Wuh-Liang Hwu ; Ni-Chung Lee

关键词：acid ¦Á-glucosidase ; enzyme replacement therapy ; glycogen storage disease type II ; newborn screening ; Pompe disease

刊名：Pediatrics Neonatology

出版年：2013

9.An improved tuning method of fractional order proportional differentiation (FOPD) controller for the path tracking control of tractors

作者：Meina Zhang ; Xiangze Lin ; Wenqing Yin

关键词：Fractional order proportion differentiation (FOPD) controller ; Tuning method ; Path tracking control ; Tractor

刊名：Biosystems Engineering

出版年：December, 2013

10.One 2D Ni(II)-based compound showing diamagnetic-paramagnetic transition

作者：Wen-yuan Xu ; Xiao-zhao Tian ; Gong-ming Sun ; Yu-mei Song ; Zi-zun Yuan ; Zhen-wei Liao ; Hai-xiao Huang ; Ming-biao Luo ; Shu-juan Liu ; Feng Luo ; ^{ecitluofeng@163.com}

关键词：Ni(II) compound ; OPDA ; Inorganic NiCl2 net ; Diamagnetic-paramagnetic transition

刊名：Inorganic Chemistry Communications

出版年：2012

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