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内部出版物
Wiley电子期刊(1)
Elsevier电子期刊(10)
在“
Elsevier电子期刊
”中,
命中:
10
条,耗时:0.0399797 秒
在所有数据库中总计命中:
11
条
1.
SGSH gene transfer in mucopolysaccharidosis type IIIA mice using canine adenovirus vectors
作者:
Adeline A. Lau
;
John
J.
Hopwood
;
Eric J. Kremer
;
Kim
M.
Hemsley
关键词:
Mucopolysaccharidosis
;
Sanfilippo syndrome
;
Canine adenovirus
;
Gene therapy
刊名:Molecular Genetics
and
Metabolism
出版年:2010
2.
Allogeneic stem cell transplantation does not improve neurological deficits in mucopolysaccharidosis type IIIA mice
作者:
Adeline A. Lau
;
Hanan Hannouche
;
Tina Rozaklis
;
Sofia Hassiotis
;
John
J.
Hopwood
;
Kim
M.
Hemsley
关键词:
Allogeneic stem cell transplantation
;
Mucopolysaccharidosis
;
Sanfilippo syndrome
;
Lysosomal storage disease
;
Mouse
刊名:Experimental Neurology
出版年:2010
3.
Effect of cisternal sulfamidase delivery in MPS IIIA Huntaway dogs—A proof of principle study
作者:
Kim
M.
Hemsley
;
Elizabeth J. Norman
;
Allison C. Crawley
;
Dyane Auclair
;
Barbara King
;
Maria Fuller
;
Debbie L. Lang
;
Caroline J. Dean
;
Robert D. Jolly
;
John
J.
Hopwood
关键词:
Sanfilippo
;
Mucopolysaccharidosis type IIIA
;
Lysosomal storage disorder
;
Cerebrospinal fluid
;
Enzyme replacement therapy
;
Intracisternal delivery
;
Canine disease model
刊名:Molecular Genetics
and
Metabolism
出版年:2009
4.
Open field locomotor activity
and
anxiety-related behaviors in mucopolysaccharidosis type IIIA mice
作者:
Adeline A. Lau
;
Allison C. Crawley
;
John
J.
Hopwood
;
Kim
M.
Hemsley
关键词:
Mucopolysaccharidosis
;
Sanfilippo syndrome
;
Elevated plus maze
;
Anxiety
;
Open field activity
;
C57BL/6
刊名:Behavioural Brain Research
出版年:2008
5.
Injection of recombinant human sulfamidase into the CSF via the cerebellomedullary cistern in MPS IIIA mice
作者:
Kim
M.
Hemsley
;
Barbara King
;
John
J.
Hopwood
关键词:
MPS IIIA
;
Lysosomal storage disorder
;
Mouse
;
CNS
;
Recombinant enzyme
;
Cerebrospinal fluid
;
Mass spectrometry
;
Neuropathology
;
Behavior
;
Humoral immune response
刊名:Molecular Genetics
and
Metabolism
出版年:2007
6.
Validation of a heparan sulfate-derived disaccharide as a marker of accumulation in murine mucopolysaccharidosis type IIIA
作者:
Barbara King
;
Peter Savas
;
Maria Fuller
;
John
Hopwood
and
Kim
Hemsley
关键词:
Lysosomal storage disorder
;
Heparan sulfate
;
Electrospray-ionization t
and
em mass spectrometry
;
Oligosaccharides
;
Mucopolysaccharidosis type IIIA
;
Mouse
;
Sulfamidase
刊名:Molecular Genetics
and
Metabolism
出版年:2006
7.
Characterization of a C57BL/6 congenic mouse strain of mucopolysaccharidosis type IIIA
作者:
Allison C. Crawley
;
Briony L. Gliddon
;
Dyane Auclair
;
Suzanne L. Brodie
;
Craig Hirte
;
Barbara M. King
;
Maria Fuller
;
Kim
M.
Hemsley
and
John
J.
Hopwood
关键词:
Animal model
;
Lysosomal storage disease
;
Mucopolysaccharidoses
;
Sanfilippo syndrome
;
Sulfamidase deficiency
;
Mouse behavior
;
Central nervous system
;
T
and
em mass spectrometry
刊名:Brain Research
出版年:2006
8.
Development of motor deficits in a murine model of mucopolysaccharidosis type IIIA (MPS-IIIA)
作者:
Hemsley
;
Kim
M.
;
Hopwood
;
John
J.
关键词:
MPS-IIIA
;
Mouse
;
Motor
;
Gait
;
Locomotion
;
Grip strength
;
Geotaxis
;
Gender
刊名:Behavioural Brain Research
出版年:2005
9.
Intracerebral injection of sulfamidase delays neuropathology in murine MPS-IIIA
作者:
Savas
;
Peter S.
;
Hemsley
;
Kim
M.
;
Hopwood
;
John
J.
关键词:
Lysosomal storage disorder
;
MPS-IIIA
;
Mucopolysaccharidosis
;
Sulfamidase
;
Mouse
;
Neurodegeneration
;
Neuropathology
;
Ubiquitin
;
GFAP
;
Brain
刊名:Molecular Genetics
and
Metabolism
出版年:2004
10.
In vitro characterization of genetically modified embryonic stem cells as a therapy for murine mucopolysaccharidosis type IIIA
作者:
Lau
;
Adeline A.
;
Hemsley
;
Kim
M.
;
Meedeniya
;
Adrian
;
Hopwood
;
John
J.
关键词:
Sulfamidase
;
Mucopolysaccharidosis
;
Lysosomal storage diseases
;
Embryonic stem cells
;
In vitro
刊名:Molecular Genetics
and
Metabolism
出版年:2004
1
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