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在“
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934,864
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在所有数据库中总计命中:
1,141,878
条
1.
Mutati
o
ns in ATP6
V
1E1
o
r ATP6V1A Cause Aut
o
s
o
mal-Recessi
v
e Cutis Laxa
作者:
Tim
V
an Damme
1
;
25
;
Thatjana Gardeitchik
2
;
3
;
25
;
Miski M
o
hamed
2
;
25
;
Sergi
o
Guerrer
o
-Castill
o
4
;
5
;
26
;
Peter Freisinger
6
;
26
;
Brecht Guillemyn
1
;
26
;
Ariana Kariminejad
7
;
26
;
Daisy Dall
o
yaux
2
;
5
;
Sanne
v
an Kraaij
2
;
5
;
Dirk J. Lefeber
5
;
8
;
Delfien Syx
1
;
W
o
uter Steyaert
1
;
Riet De Rycke
9
;
10
;
Alexander H
o
ischen
3
;
Erik-Jan Kamsteeg
3
;
Sunnie Y. W
o
ng
11
;
M
o
nique
v
an Scherpenzeel
5
;
8
;
Payman Jamali
12
;
Ulrich Brandt
4
;
5
;
Le
o
Nijtmans
4
;
5
;
G. Christ
o
ph K
o
renke
13
;
Brian H.Y. Chung
14
;
Christ
o
pher C.Y. Mak
14
;
Ingrid Hausser
15
;
Uwe K
o
rnak
16
;
17
;
Bj&
o
uml
;
rn Fischer-Zirnsak
16
;
17
;
Tim M. Str
o
m
18
;
Th
o
mas Meitinger
18
;
Yasemin Alanay
19
;
Gulen E. Utine
20
;
Peter K.C. Leung
14
;
Sia
v
ash Ghaderi-S
o
hi
7
;
Paul C
o
ucke
1
;
S
o
fie Sym
o
ens
1
;
Anne De Paepe
1
;
Christian Thiel
21
;
T
o
bias B. Haack
18
;
22
;
23
;
Fransiska Malfait
1
;
27
;
E
v
a M
o
ra
v
a
11
;
24
;
27
;
Bert Callewaert
1
;
27
;
bert.callewaert@ugent.be
;
R
o
n A. We
v
ers
5
;
27
;
r
o
n.we
v
ers@radb
o
udumc.nl
关键词:
V
-ATPase
;
ATP6
V
1E1
;
ATP6
V
1A
;
cutis laxa
;
aut
o
s
o
mal recessi
v
e
;
ARCL2
;
c
o
ngenital dis
o
rder
o
f glyc
o
sylati
o
n
;
CDG
;
G
o
lgi apparatus
;
cellular trafficking
刊名:The American J
o
urnal
o
f Human Genetics
出版年:2017
2.
C
o
mparing the luminescence pr
o
cesses
o
f Y
V
O
4
:Eu and c
o
re-shell YVO
4
@YF
3
nan
o
crystals with bulk-YVO
4
:Eu
作者:
L. Shirmane
a
;
liana.shirmane@gmail.c
o
m" class="auth_mail" title="E-mail the c
o
rresp
o
nding auth
o
r
;
C. Feldmann
b
;
V
. Pankrat
ov
a
;
c
;
d
;
v
ladimirs.pankrat
ov
s@
o
ulu.fi" class="auth_mail" title="E-mail the c
o
rresp
o
nding auth
o
r
;
v
pank@latnet.l
v
" class="auth_mail" title="E-mail the c
o
rresp
o
nding auth
o
r
;
v
ladimirs.pankrat
ov
s@maxi
v
.se" class="auth_mail" title="E-mail the c
o
rresp
o
nding auth
o
r
关键词:
Y
VO
4
;
Eu3+
;
Nan
o
ph
o
sph
o
rs
;
C
o
re-Shelled nan
o
particles
;
Luminescence
;
Synchr
o
tr
o
n radiati
o
n
刊名:Physica B: Physics
o
f C
o
ndensed Matter
出版年:2017
3.
A c
o
mmercial p
o
rcine circ
ov
irus (PCV) type 2a-based
v
accine reduces PCV2d
v
iremia and shedding and pre
v
ents PCV2d transmissi
o
n t
o
naï
v
e pigs under experimental c
o
nditi
o
ns
作者:
Tanja
O
priessnig
a
;
b
;
Tanja.
O
priessnig@r
o
slin.ed.ac.uk
;
Cha
o
-Ting Xia
o
b
;
c
;
Patrick G. Halbur
b
;
Priscilla F. Gerber
a
;
Shann
o
n R. Matzinger
d
;
Xiang-Jin Meng
d
关键词:
P
o
rcine circ
ov
irus
;
PC
V
2
;
PC
V
2d
;
V
accinati
o
n
;
V
accine efficacy
;
Transmissi
o
n
刊名:
V
accine
出版年:2017
4.
B
o
ne tissue resp
o
nse induced by bi
o
acti
v
e p
o
lymer functi
o
nalized Ti6Al4V surfaces: In
v
itr
o
and in
v
i
vo
study
作者:
Helena P. Felgueiras
a
;
felgueiras.helena@gmail.c
o
m
;
Adeline Decambr
o
n
b
;
c
;
Mathieu Manasser
o
b
;
c
;
L
o
uise Tulasne
c
;
Margaret D.M. E
v
ans
d
;
V
é
;
r
o
nique
V
iateau
b
;
c
;
V
é
;
r
o
nique Mig
o
nney
a
关键词:
Ti6Al4
V
;
P
o
ly(s
o
dium styrene sulf
o
nate) grafting
;
C
o
llagen type I
;
B
o
ne m
o
rph
o
genetic pr
o
tein-2
;
O
ste
o
genesis
;
O
sse
o
integrati
o
n
刊名:J
o
urnal
o
f C
o
ll
o
id and Interface Science
出版年:2017
5.
Characterizati
o
n
o
f culture filtrate pr
o
teins R
v
1197 and R
v
1198
o
f ESAT-6 family fr
o
m Myc
o
bacterium tubercul
o
sis H37R
v
作者:
Himanshu Pandey
a
;
Sarita Tripathi
a
;
Kanchan Sri
v
asta
v
a
c
;
Dinesh K. Tripathi
b
;
Mrigank Sri
v
asta
v
a
d
;
Surya Kant
c
;
Kish
o
re K. Sri
v
asta
v
a
b
;
kish
o
re@cdri.res.in
;
Ashish Ar
o
ra
a
;
ashish_ar
o
ra@cdri.res.in
关键词:
Myc
o
bacterium tubercul
o
sis
;
ESAT-6 family
;
R
v
1197
;
R
v
1198
;
Ser
o
reacti
v
ity
;
V
accine
刊名:Bi
o
chimica et Bi
o
physica Acta (BBA) - General Subjects
出版年:2017
6.
Semic
o
nducting pr
o
perties
o
f c
o
ld sintered
V
2
O
5
ceramics and C
o
-sintered V
2
O
5
-PEDOT:PSS c
o
mp
o
sites
作者:
Jing Gu
o
a
;
jug34@psu.edu
;
Hanzheng Gu
o
a
;
Dam
oo
n S
o
hrabi Baba Heidary
a
;
Shuichi Funahashi
a
;
b
;
Cli
v
e A. Randall
a
;
car4@psu.edu
关键词:
C
o
ld sintering pr
o
cess
;
O
xide semic
o
nduct
o
r
;
V
2
O
5
;
V
2
O
5-PEDOT
;
PSS c
o
mp
o
site
;
Metal-insulat
o
r transiti
o
n
刊名:J
o
urnal
o
f the Eur
o
pean Ceramic S
o
ciety
出版年:2017
7.
V
γ1
+
γδT, early cardiac infiltrated innate p
o
pulati
o
n d
o
minantly pr
o
ducing IL-4, pr
o
tect mice against CVB3 my
o
carditis by m
o
dulating IFNγ
+
T resp
o
nse
作者:
Fangfang Wan
1
;
Kepeng Yan
1
;
Dan Xu
;
Qian Qian
;
Hui Liu
;
Min Li
;
Wei Xu
;
xuweifd828@126.c
o
m
关键词:
V
iral my
o
carditis
;
C
V
B3
;
γδT
;
V
γ1
;
IL-4
刊名:M
o
lecular Immun
o
l
o
gy
出版年:2017
8.
LiMnP
O
4
·Li
3
V
2
(PO
4
)
3
c
o
mp
o
site cath
o
de material deri
v
ed fr
o
m Mn(VO
3
)
2
nan
o
sheet precurs
o
r
作者:
Zhih
o
ng Lei
a
;
Jun Yang
a
;
Yang He
b
;
Yuyan Sha
o
c
;
Sc
o
tt X. Ma
o
b
;
Ch
o
ngming Wang
c
;
Yanna Nuli
a
;
Jiulin Wang
a
;
wangjiulin@sjtu.edu.cn
关键词:
LiMnP
O
4
;
Li3
V
2(P
O
4)3
;
Mn(
VO
3)2
;
Cath
o
de material
;
Lithium i
o
n battery
刊名:J
o
urnal
o
f All
o
ys and C
o
mp
o
unds
出版年:2017
9.
Electr
o
p
o
lishing and electr
o
p
o
lishing-related all
o
wances f
o
r p
o
wder bed selecti
v
ely laser-melted Ti-6Al-4V all
o
y c
o
mp
o
nents
作者:
V
. Urlea
;
V
. Brail
ov
ski
;
v
.brail
ov
@gmail.c
o
m
;
v
ladimir.brail
ov
ski@etsmtl.ca
关键词:
Additi
v
e manufacturing
;
Selecti
v
e laser melting
;
Build
o
rientati
o
n
;
Surface finish
;
Electr
o
p
o
lishing all
o
wances
;
Ti-6Al-4
V
刊名:J
o
urnal
o
f Materials Pr
o
cessing Techn
o
l
o
gy
出版年:2017
10.
U
V
-B Percei
v
ed by the UVR8 Ph
o
t
o
recept
o
r Inhibits Plant Therm
o
m
o
rph
o
genesis
作者:
Sc
o
tt Hayes
1
;
2
;
6
;
Ashut
o
sh Sharma
1
;
6
;
D
o
nald P. Fraser
1
;
Martine Tre
v
isan
3
;
C. Kester Cragg-Barber
1
;
Eleni Ta
v
rid
o
u
4
;
Christian Fankhauser
3
;
Gareth I. Jenkins
5
;
Keara A. Franklin
1
;
7
;
kerry.franklin@brist
o
l.ac.uk
关键词:
U
V
-B
;
Arabid
o
psis
;
U
V
R8
;
high temperature
;
auxin
;
hyp
o
c
o
tyl
;
HFR1
;
PIF4
刊名:Current Bi
o
l
o
gy
出版年:2017
1
2
3
4
5
6
7
8
9
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