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内部出版物
SpringerLink电子期刊(25)
Elsevier电子期刊(31)
ACS电子期刊(2)
在“
Elsevier电子期刊
”中,
命中:
31
条,耗时:0.0869599 秒
在所有数据库中总计命中:
58
条
1.
Partial correction of neutrophil dysfunction by oral galactose therapy in
glycogen
storage
disease
type
Ib
作者:
Rudolf Letkemann
a
;
r.letkemann@uni-muenster.de
;
Helmut Wittkowski
b
;
helmut.wittkowski@ukmuenster.de
;
Aristotelis Antonopoulos
c
;
a.antonopoulos@imperial.ac.uk
;
Teodor Podskabi
d
;
metabolic-genetic-
disease
@gmx.de
;
Stuart M. Haslam
c
;
s.haslam@imperial.ac.uk
;
Dirk Fö
;
ll
b
;
dfoell@uni-muenster.de
;
Anne Dell
c
;
a.dell@imperial.ac.uk
;
Thorsten Marquardt
a
;
marquat@uni-muenster.de
关键词:
CHAPS
;
3-[(3-cholamidopropyl)dimethylammonio]-1-propanesulfonate
;
CDG
;
congenital disorder of glycosylation
;
DHR
;
dihydrorhodamine
;
E. coli
;
Escherichia coli
;
EDTA
;
ethylenediaminetetraacetic acid
;
FICT
;
fluorescein isothiocyanate
;
fMLP
;
formyl-methionyl-leucyl-phenylalanine
;
G1P
;
glucose 1-phosphate
;
G6P
;
glucose 6-phosphate
;
G6PC
;
glucose 6-phosphate catabolic
;
G6PT
;
glucose 6-phosphate transporter
;
GCSF
;
granulocyte-colony stimulating factor
;
GSD-
Ib
;
glycogen
storage
disease
type
Ib
;
HMPS
;
he
刊名:International Immunopharmacology
出版年:2017
2.
Glycogen
storage
disease
type
Ib
neutrophils exh
ib
it impaired cell adhesion and migration
作者:
Goo-Young Kim
a
;
Young Mok Lee
a
;
Joon Hyun Kwon
a
;
Hyun Sik Jun
b
;
toddjun@korea.ac.kr
;
Janice Chou
a
;
chouja@mail.nih.gov
关键词:
Glucose-6-phosphate transporter
;
CD11a
;
CD11b
;
Neutrophil adhesion
;
Migration
刊名:Biochemical and Biophysical Research Communications
出版年:2017
3.
Rapid height growth after liver transplantation in adulthood
作者:
Balá
;
zs Szili
a
;
szil
ib
@med.semmelweis-univ.hu" class="auth_mail" title="E-mail the corresponding author
;
Dé
;
nes Gö
;
rö
;
g
b
;
gorogd@freemail.hu" class="auth_mail" title="E-mail the corresponding author
;
Zsuzsanna Gerlei
b
;
gerleizs@gmail.com" class="auth_mail" title="E-mail the corresponding author
;
Gabriella Győri
c
;
gyoriga@gmail.com" class="auth_mail" title="E-mail the corresponding author
;
Pé
;
ter Lakatos
a
;
lakatos.peter@med.semmelweis-univ.hu" class="auth_mail" title="E-mail the corresponding author
;
Istvá
;
n Taká
;
cs
a
;
takacs.istvan@med.semmelweis-univ.hu" class="auth_mail" title="E-mail the corresponding author
关键词:
G6P
;
glucose-6-phosphatase
;
GH
;
growth hormone
;
GSD
;
glycogen
-
storage
disease
;
IGF
;
insulin-like growth factor
;
BMD
;
bone mineral density
;
SDS
;
standard deviation score
刊名:Growth Hormone & IGF Research
出版年:2016
4.
Mouse model of
glycogen
storage
disease
type
III
作者:
Kai-Ming Liu
a
;
b
;
Jer-Yuarn Wu
a
;
Yuan-Tsong Chen
a
;
c
;
chen0010@
ib
ms.sinica.edu.tw" class="auth_mail
关键词:
GSD III
;
Glycogen
storage
disease
type
III
;
GDE
;
Glycogen
debranching enzyme
;
Mouse model
刊名:Molecular Genetics and Metabolism
出版年:April, 2014
5.
Molecular characterization of hepatocellular adenomas developed in patients with
glycogen
storage
disease
type
I
作者:
Julien Calderaro
1
;
2
;
3
;
Philippe Labrune
4
;
Guillaume Morcrette
1
;
2
;
Sandra Rebouissou
1
;
2
;
Dominique Franco
5
;
Sophie Pré
;
vot
6
;
Alberto Quaglia
7
;
Pierre Bedossa
8
;
Louis L
ib
brecht
9
;
Luigi Terracciano
10
;
G. Peter A. Smit
11
;
Paulette Bioulac-Sage
12
;
13
;
Jessica Zucman-Rossi
1
;
2
;
14
;
Jessica.zucman-rossi@inserm.fr
关键词:
bHCA
;
CTNNB1 mutated adenoma
;
GSD
;
glycogen
storage
disease
type
I
;
HCA
;
hepatocellular adenoma
;
HCC
;
hepatocellular carcinoma
;
H-HCA
;
HNF1A-inactivated adenoma
;
IHCA
;
inflammatory adenoma
;
UHCA
;
unclassified adenoma
刊名:Journal of Hepatology
出版年:2013
6.
Noncompaction myocardium in association with
type
Ib
glycogen
storage
disease
作者:
Benjamin Goeppert
;
Martin Lindner
;
Monika Nadja Vogel
;
Arne Warth
;
Albrecht Stenzinger
;
Marcus Renner
;
Philipp Schnabel
;
Peter Schirmacher
;
Frank Autschbach
;
Wilko Weichert
关键词:
Noncompaction myocardium
;
Type
Ib
glycogen
storage
disease
刊名:Pathology - Research and Practice
出版年:2012
7.
Liver cirrhosis in
glycogen
storage
disease
Ib
作者:
Fabian Baertling
a
;
Fabian.Baertling@med.uni-duesseldorf.de
;
Ertan Mayatepek
a
;
Mayatepek@med.uni-duesseldorf.de
;
Patrick Gerner
b
;
Patrick.Gerner@uk-essen.de
;
Hideo A. Baba
c
;
Hideo.Baba@uk-essen.de
;
Julia Franzel
a
;
Julia.Franzel@med.uni-duesseldorf.de
;
Andrea Schlune
a
;
Andrea.Schlune@med.uni-duesseldorf.de
;
Thomas Meissner
a
;
Thomas.Meissner@med.uni-duesseldorf.de
关键词:
AIH
;
autoimmune hepatitis
;
ANAs
;
anti-nuclear-ant
ib
odies
;
AP
;
alkaline phosphatase
;
GCSF
;
granulocyte colony stimulating factor
;
¦Ã-GT
;
¦Ã-glutamyltranspeptidase
;
GOT
;
glutamic oxaloacetic transaminase
;
GPT
;
glutamic pyruvic transaminase
;
GSD
;
glycogen
st
刊名:Molecular Genetics and Metabolism
出版年:2013
8.
Natural History of Hepatocellular Adenoma Formation in
Glycogen
Storage
Disease
Type
I
作者:
David Q. Wang
;
MD
;
Laurie M. Fiske
;
BS
;
Caroline T. Carreras
;
David A. Weinstein
;
MD
;
MMSc
;
weinsda@peds.ufl.edu
关键词:
BMI
;
Body mass index
;
ESGSD I
;
European Study on
Glycogen
Storage
Disease
Type
I
;
GSD I
;
Glycogen
storage
disease
type
I
;
GSD Ia
;
Glycogen
storage
disease
type
Ia
;
GSD
Ib
;
Glycogen
storage
disease
type
Ib
;
HCA
;
Hepatocellular adenoma
刊名:The Journal of Pediatrics
出版年:2011
9.
The SLC37 family of phosphate-linked sugar phosphate antiporters
作者:
Janice Y. Chou
a
;
chouja@mail.nih.gov
;
Hyun Sik Jun
a
;
Brian C. Mansfield
a
;
b
关键词:
SLC37
;
Sugar phosphate exchanger
;
Glucose-6-phosphate transporter
;
Endoplasmic reticulum
;
Glycogen
storage
disease
type
Ib
;
Glucose-6-phosphatase
刊名:Molecular Aspects of Medicine
出版年:2013
10.
Glycogen
Storage
Disease
Type
Ib
: The First Case in Taiwan
作者:
Hui-Ju Hsiao
;
Hsiu-Hao Chang
;
Wuh-Liang Hwu
;
Ching-Wan Lam
;
Ni-Chung Lee
;
Yin-Hsiu Chien
关键词:
G-CSF
;
glycogen
storage
disease
type
Ib
;
neutropenia
;
recurrent infection
刊名:Pediatrics Neonatology
出版年:2009
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