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内部出版物
SpringerLink电子期刊(6)
Elsevier电子期刊(14)
在“
Elsevier电子期刊
”中,
命中:
14
条,耗时:小于0.01 秒
在所有数据库中总计命中:
20
条
1.
The hsa-miR-125a/hsa-let-7e/hsa-miR-99b cluster is potentially implicated in Cystic Fibrosis pathogenesis
作者:
Marie-Laure Endale Ahanda
a
;
Thierry Bienvenu
b
;
Isabelle Sermet-Gaudelus
c
;
Laurent Mazzolini
d
;
Aleksander Edelman
c
;
Rima Zoorob
e
;
Noé
;
lie Davezac
f
;
关键词:
Cystic Fibrosis
;
MicroRNAs
;
CFTR
;
SNPs
刊名:Journal of Cystic Fibrosis
出版年:2015
2.
A statistical model to predict one-year risk of death in patients with cystic fibrosis
作者:
Shawn D. Aaron
a
;
saaron@ohri.ca" class="auth_mail" title="E-mail the corresponding author
;
Anne L. Stephenson
b
;
Donald W. Cameron
a
;
George A. Whitmore
a
;
c
关键词:
Cystic fibrosis
;
Health index
;
Mortality
;
Registry data
;
Risk scoring tool
;
Threshold regression
刊名:Journal of Clinical Epidemiology
出版年:2015
3.
42 Microbiologic bacterial agents in a young cystic fibrosis population
作者:
A.C. Freitas
a
;
J.O. Neves
b
;
T. Barbosa
a
;
V. Lopes
b
;
H. Ramos
b
;
V. Senra
a
;
H. Rocha
a
刊名:Journal of Cystic Fibrosis
出版年:2015
4.
Osteopenia in Cftr-
deltaF508
mice
作者:
José
;
e Paradis
;
Martina Wilke
;
Christina K. Haston
关键词:
Bone disease
;
Genetically modified mouse
;
Cftr
;
deltaF508
;
Femur
刊名:Journal of Cystic Fibrosis
出版年:2010
5.
Bone loss in adults with cystic fibrosis: Prevalence, associated factors, and usefulness of biological markers
作者:
Isabelle Legroux-Gé
;
rot
a
;
isabelle.legroux@chru-lille.fr
;
Sylvie Leroy
b
;
Caroline Prudhomme
a
;
Thierry Perez
b
;
René
;
Marc Flipo
a
;
Benoî
;
t Wallaert
b
;
Bernard Cortet
a
关键词:
Cystic fibrosis
;
Osteoporosis
;
Osteopenia
;
Bone turnover markers
刊名:Joint Bone Spine
出版年:2012
6.
Functional Rescue of
DeltaF508
-CFTR by Peptides Designed to Mimic Sorting Motifs
作者:
Patrick Kim Chiaw
;
Ling-Jun Huan
;
Stephane Gagnon
;
Diane Ly
;
Neil Sweezey
;
Daniela Rotin
;
Charles M. Deber
;
Christine E. Bear
刊名:Chemistry & Biology
出版年:2009
7.
Report of two patients with associated conditions in addition to cystic fibrosis
作者:
Supriya K. Jambhekar
;
John L. Carroll
;
Steven Keiles
关键词:
Cystic fibrosis
;
Mutation
;
Genetics
;
Gene sequence analysis
;
Cystic fibrosis transmembrane conductance regulator
;
Associated conditions
;
Crohn's disease
;
Rubinstein–
;
Taybi syndrome
刊名:Journal of Cystic Fibrosis
出版年:2010
8.
FROM “EVOCATIVE” SYMPTOMS TO GENOTYPE
DELTAF508
/E831X
作者:
C. Di Girgenti
;
L. Virruso
;
R. Messineo
;
A. Cannuscio
;
L. Termini
;
F. Pardo
刊名:Journal of Cystic Fibrosis
出版年:2008
9.
31 Rescue of
deltaF508
CFTR in CFBE41o- cells is dependent on actin cytoskeleton interaction with ezrin and NHERF1
作者:
L. Guerra
;
S.M. Riccardi
;
M. Favia
;
T. Fanelli
;
G. Busco
;
R.A. Cardone
;
S.J. Reshkin
;
S. Carrabino
;
M. Conese
;
V. Casavola
刊名:Journal of Cystic Fibrosis
出版年:2007
10.
28 Curcumin rescues
deltaF508
-CFTR via the keratin 18 network
作者:
J. Lipecka
;
C. Norez
;
N. Bensalem
;
M. Baudouin-Legros
;
G. Planelles
;
E. Becq
;
A. Edelman
;
N. Davezac
刊名:Journal of Cystic Fibrosis
出版年:2006
1
2
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