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Wiley电子期刊(9)
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ACS电子期刊(136)
SpringerLink电子期刊(223)
Elsevier电子期刊(392)
在“
Elsevier电子期刊
”中,
命中:
392
条,耗时:0.052939 秒
在所有数据库中总计命中:
765
条
1.
Efficacy of bezafibrate on fibroblasts of
glutaric
acid
emia type II patients evaluated using an in vitro probe acylcarnitine assay
作者:
Kenji Yamada
a
;
k-yamada@med.shimane-u.ac.jp
;
Hironori Kobayashi
a
;
Ryosuke Bo
a
;
b
;
Jamiyan Purevsuren
a
;
Yuichi Mushimoto
a
;
Tomoo Takahashi
a
;
Yuki Hasegawa
a
;
Takeshi Taketani
a
;
Seiji Fukuda
a
;
Seiji Yamaguchi
a
关键词:
Bezafibrate
;
Glutaric
acid
emia type II
;
Multiple acyl-CoA dehydrogenase deficiency
;
In vitro probe assay
;
Fatty
acid
oxidation disorders
刊名:Brain and Development
出版年:2017
2.
Determination and correlation of solid-liquid phase equilibrium and phase diagram for multicomponent system of mixed dibasic
acid
s. (III) Ternary system of succinic
acid
+
glutaric
acid
+ ethanol system
作者:
Rongrong Li
a
;
Li Lin
a
;
Wenjuan Feng
a
;
Jiayu Xu
a
;
Cunbin Du
b
;
Hongkun Zhao
b
;
hkzhao@yzu.edu.cn
关键词:
Solid-liquid phase equilibrium
;
Phase diagram
;
Succinic
acid
;
Glutaric
acid
;
Ethanol
刊名:The Journal of Chemical Thermodynamics
出版年:2017
3.
Determination and correlation of solid-liquid phase equilibrium and phase diagram for multicomponent system of mixed dibasic
acid
s. (I) Ternary system of adipic
acid
+
glutaric
acid
+ ethanol system
作者:
Long Meng
;
Jian Xu
;
Cun Bin Du
;
Shuo Han
;
Ren Jie Xu
;
Jian Wang
;
Hong Kun Zhao
;
hkzhao@yzu.edu.cn" class="auth_mail" title="E-mail the corresponding author
关键词:
Solid&ndash
;
liquid phase equilibrium
;
Phase diagram
;
Adipic
acid
;
Glutaric
acid
;
Ethanol
刊名:Fluid Phase Equilibria
出版年:2016
4.
Clinical and molecular investigation in Chinese patients with
glutaric
acid
uria type I
作者:
Yanghui Zhang
a
;
Haoxian Li
a
;
b
;
Ruiyu Ma
a
;
Libin Mei
a
;
Xianda Wei
a
;
Desheng Liang
a
;
b
;
liangdesheng@sklmg.edu.cn" class="auth_mail" title="E-mail the corresponding author
;
Lingqian Wu
a
;
b
;
wulingqian@sklmg.edu.cn" class="auth_mail" title="E-mail the corresponding author
关键词:
Glutaric
acid
uria type I
;
GCDH
;
Splice site mutation
;
Newborn screening
刊名:Clinica Chimica Acta
出版年:2016
5.
Preparation and modification of water-blown porous biodegradable polyurethane foams with palm oil-based polyester polyol
作者:
Wei Seng Ng
a
;
Choy Sin Lee
b
;
Cheng Hock Chuah
a
;
Sit-Foon Cheng
a
;
sfcheng@um.edu.my
关键词:
Palm oil-based
;
Polyester polyol
;
Polyurethane
;
Water-blown
;
Biodegradable polymers
刊名:Industrial Crops and Products
出版年:2017
6.
A non-cyanide route for
glutaric
acid
synthesis from oxidation of cyclopentene in the ionic liquid media
作者:
Majid Vafaeezadeh
;
majidvafaeezadeh@alum.sharif.edu" class="auth_mail" title="E-mail the corresponding author
;
majidvafaeezadeh@yahoo.com" class="auth_mail" title="E-mail the corresponding author
;
Mohammad Mahmoodi Hashemi
关键词:
Glutaric
acid
;
Clean oxidation
;
H2O2
;
Ionic liquid
;
Green chemistry
;
Cyclopentene
刊名:Process Safety and Environmental Protection
出版年:2016
7.
Clinical, biochemical and molecular investigation of adult-onset
glutaric
acid
emia type II: Characteristics in comparison with pediatric cases
作者:
Kenji Yamada
a
;
k-yamada@med.shimane-u.ac.jp" class="auth_mail" title="E-mail the corresponding author
;
Hironori Kobayashi
a
;
Ryosuke Bo
a
;
Tomoo Takahashi
a
;
Jamiyan Purevsuren
a
;
Yuki Hasegawa
a
;
Takeshi Taketani
a
;
Seiji Fukuda
a
;
Takuya Ohkubo
b
;
Takanori Yokota
b
;
Mutsufusa Watanabe
c
;
Taiji Tsunemi
d
;
Hidehiro Mizusawa
e
;
Hiroshi Takuma
f
;
Ayako Shioya
f
;
Akiko Ishii
f
;
Akira Tamaoka
f
;
Yosuke Shigematsu
g
;
Hideo Sugie
h
;
Seiji Yamaguchi
a
关键词:
Multiple acyl-CoA dehydrogenase deficiency (
glutaric
acid
emia type II)
;
Adult onset
;
Myopathy
;
Serum acylcarnitine
;
Immunoblotting
;
In vitro probe acylcarnitine assay
刊名:Brain and Development
出版年:2016
8.
Phase equilibria of CH
4
and CO
2
hydrates formed from aqueous solutions of
glutaric
acid
and malonic
acid
作者:
Jong-Ho Cha
a
;
Seong-Pil Kang
b
;
spkang@kier.re.kr" class="auth_mail" title="E-mail the corresponding author
;
Songlee Han
b
;
c
;
Jeong Won Kang
d
;
e
;
jwkang@ut.ac.kr" class="auth_mail" title="E-mail the corresponding author
;
Ki-Sub Kim
a
;
kks1114@ut.ac.kr" class="auth_mail" title="E-mail the corresponding author
关键词:
Di-carboxylic
acid
;
Gas hydrate
;
Inhibitor
;
Phase equilibrium
;
Flow assurance
刊名:Fluid Phase Equilibria
出版年:2016
9.
Spectrum of mutations in Glutaryl-CoA dehydrogenase gene in
glutaric
acid
uria type I - Study from South India
作者:
A. Radha Rama Devi
a
;
c
;
radharamadevi@gmail.com" class="auth_mail" title="E-mail the corresponding author
;
Vakkalagadda A. Ramesh
d
;
e
;
H.A. Nagarajaram
d
;
S.P.S. Satish
c
;
U. Jayanthi
c
;
Lokesh Lingappa
b
关键词:
Glutaric
acid
uria
;
Glutaryl-CoA dehydrogenase
;
Metabolic disease
;
Novel mutation
;
Movement disorders
刊名:Brain and Development
出版年:2016
10.
The M405V allele of the glutaryl-CoA dehydrogenase gene is an important marker for
glutaric
acid
uria type I (GA-I) low excretors
作者:
Lori-Anne P. Schillaci
a
;
1
;
Carol L. Greene
b
;
Erin Strovel
b
;
Jessica Rispoli-Joines
b
;
Elaine Spector
c
;
Michael Woontner
c
;
Gunter Scharer
c
;
Gregory M. Enns
d
;
Renata Gallagher
e
;
Arthur B. Zinn
a
;
g
;
Shawn E. McCandless
a
;
f
;
g
;
Charles L. Hoppel
h
;
i
;
Stephen I. Goodman
c
;
Jirair K. Bedoyan
a
;
f
;
g
;
1
;
jirair.bedoyan@uhhospitals.org" class="auth_mail" title="E-mail the corresponding author
关键词:
GCDH
;
Glutaryl-CoA dehydrogenase
;
Glutaric
acid
uria
;
Low excretor
;
Newborn screen
;
Urinary acylcarnitines
刊名:Molecular Genetics and Metabolism
出版年:2016
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