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内部出版物
知网期刊论文(1)
在“
Elsevier电子期刊
”中,
命中:
9
条,耗时:小于0.01 秒
在所有数据库中总计命中:
1
条
1.
Transcription Factor EB Controls Metabolic Flexibility during Exercise
作者:
Gelsomina Mansueto
1
;
Andrea Armani
2
;
Carlo Viscomi
3
;
4
;
Luca D&rsquo
;
Orsi
1
;
Rossella De Cegli
1
;
Elena V. Polishchuk
1
;
Costanza
Lamperti
4
;
Ivano Di Meo
4
;
Vanina Romanello
2
;
5
;
Silvia Marchet
4
;
Pradip K. Saha
6
;
Haihong Zong
7
;
8
;
Bert Blaauw
2
;
Francesca Solagna
2
;
Caterina Tezze
2
;
Paolo Grumati
9
;
Paolo Bonaldo
9
;
Jeffrey E. Pessin
8
;
Massimo Zeviani
3
;
4
;
Marco Sandri
1
;
2
;
5
;
13
;
marco.sandri@unipd.it
;
Andrea Ballabio
1
;
10
;
11
;
12
;
ballabio@tigem.it
关键词:
TFEB
;
autophagy
;
exercise
;
glucose
;
mitochondria
;
diabetes
;
mitochondrial fusion
;
PGC1alpha
;
metabolic flexibility
;
insulin
刊名:Cell Metabolism
出版年:2017
2.
Response to: Mitochondrial neuropathy affects peripheral and cranial nerves and is primary or secondary or both
作者:
Mancuso Michelangelo
;
mancusomichelangelo@gmail.com" class="auth_mail" title="E-mail the corresponding author
;
Orsucci Daniele
;
Angelini Corrado
;
Bertini Enrico
;
Bruno Claudio
;
Carelli Valerio
;
Giacomo P Comi
;
Filosto Massimiliano
;
Lamperti
Costanza
;
Moggio Maurizio
;
Mongini Tiziana
;
Moroni Isabella
;
Tonin Paola
;
Toscano Antonio
;
Siciliano Gabriele
;
on behalf of the Nation-wide Italian Collaborative Network of Mitochondrial Diseases
刊名:Neuromuscular Disorders
出版年:2016
3.
NAD
+
-Dependent Activation of Sirt1 Corrects the Phenotype in a Mouse Model of Mitochondrial Disease
作者:
Raffaele Cerutti
1
;
8
;
Eija Pirinen
2
;
3
;
Costanza
Lamperti
1
;
Silvia Marchet
1
;
Anthony A. Sauve
4
;
Wei Li
4
;
Valerio Leoni
5
;
Eric A. Schon
6
;
Franç
;
oise Dantzer
7
;
Johan Auwerx
2
;
Carlo Viscomi
1
;
8
;
cfv23@mrc-mbu.cam.ac.uk" class="auth_mail
;
Massimo Zeviani
1
;
8
;
mdz21@mrc-mbu.cam.ac.uk" class="auth_mail
刊名:Cell Metabolism
出版年:3 June 2014
4.
In Vivo Correction of COX Deficiency by Activation of the AMPK/PGC-1α Axis
作者:
Carlo Viscomi
1
;
4
;
Emanuela Bottani
1
;
4
;
Gabriele Civiletto
1
;
Raffaele Cerutti
1
;
Maurizio Moggio
2
;
Gigliola Fagiolari
2
;
Eric
;
A. Schon
3
;
Costanza
Lamperti
1
;
Massimo Zeviani
1
;
zeviani@istituto-besta.it"" rel=""nofollow
刊名:Cell Metabolism
出版年:2011
5.
Severe X-Linked Mitochondrial Encephalomyopathy Associated with a Mutation in Apoptosis-Inducing Factor
作者:
Daniele Ghezzi
;
Irina Sevrioukova
;
Federica Invernizzi
;
Costanza
Lamperti
;
Marina Mora
;
Pio D'Adamo
;
Francesca Novara
;
Orsetta Zuffardi
;
Graziella Uziel
;
Massimo Zeviani
刊名:The American Journal of Human Genetics
出版年:2010
6.
Inclusion body myopathy and frontotemporal dementia caused by a novel VCP
作者:
Anna Bersano
;
Roberto Del Bo
;
Costanza
Lamperti
;
Serena Ghezzi
;
Gigliola Fagiolari
;
Francesco Fortunato
;
Elena Ballabio
;
Maurizio Moggio
;
Livia C
;
elise
;
Daniela Galimberti
;
Roberta Virgilio
;
Silvia La
关键词:
Inclusion body myopathy
;
Frontotemporal dementia
;
Valosin-containing protein
刊名:Neurobiology of Aging
出版年:2009
7.
The Mitochondrial Disulfide Relay System Protein GFER Is Mutated in Autosomal-Recessive Myopathy with Cataract and Combined Respiratory-Chain Deficiency
作者:
Alessio Di Fonzo
;
Dario Ronchi
;
Tiziana Lodi
;
Elisa Fassone
;
Marco Tigano
;
Costanza
Lamperti
;
Stefania Corti
;
Andreina Bordoni
;
Francesco Fortunato
;
Monica Nizzardo
;
Laura Napoli
;
Chiara Donadoni
;
Sabrina Salani
;
Francesca Saladino
;
Maurizio Moggio
;
Nereo Bresolin
;
Iliana Ferrero
;
Giacomo P. Comi
刊名:The American Journal of Human Genetics
出版年:2009
8.
Congenital muscular dystrophy with muscle inflammation alpha dystroglycan glycosylation defect and no mutation in FKRP gene
作者:
Costanza
Lamperti
;
Rachele Cagliani
;
Patrizia Ciscato
;
Isabella Moroni
;
Maurizio Viri
;
Antonio Romeo
;
Gigliola Fagiolari
;
Alessandro Prelle
;
Giacomo Pietro Comi
;
Nereo Bresolin and Maurizio Moggio
关键词:
α
;
-Dystroglycan
;
Congenital muscular dystrophy
;
Glycosylation
;
Fukutin-related protein
刊名:Journal of the Neurological Sciences
出版年:2006
9.
A case of CPT deficiency, homoplasmic mtDNA mutation and ragged red fibers at muscle biopsy
作者:
Monica Sciacco
;
Alessandro Prelle
;
Gigliola Fagiolari
;
Andreina Bordoni
;
Marco Crimi
;
Alessio Di Fonzo
;
Patrizia Ciscato
;
Costanza
Lamperti
;
Elisabetta D'Adda
;
Stefano Jann
et al.
关键词:
Myoglobinuria
;
CPT deficiency
;
Mitochondrial disorder
;
RRFs
刊名:Journal of the Neurological Sciences
出版年:2005
1
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