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内部出版物
CNKI学位论文(7)
知网期刊论文(5)
在“
Elsevier电子期刊
”中,
命中:
6
条,耗时:小于0.01 秒
在所有数据库中总计命中:
12
条
1.
Clinical follow-up in a group of Gaucher type I patients switching enzyme replacement therapy from imiglucerase to velaglucerase
作者:
Bruno Bembi
;
Annalisa Sechi
;
Andrea Dardis
;
Laura Deroma
;
Daniela Macor
;
Giulia Liva
;
Giovanni
Ciana
刊名:Molecular Genetics and Metabolism
出版年:2013
2.
Biochemical and molecular findings in a patient with myoclonic epilepsy due to a mistarget of the β-glucosidase enzyme
作者:
Andrea Dardis
;
Mirella Filocamo
;
Serena Grossi
;
Giovanni
Ciana
;
Silvana Franceschetti
;
Silvia Dominissini
;
Guido Rubboli
;
Maya Di Rocco
;
Bruno Bembi
关键词:
Myoclonus
;
β
;
-Glucosidase
;
LIMP-2 deficiency
刊名:Molecular Genetics and Metabolism
出版年:2009
3.
13. Enzyme replacement therapy with Alglucosidase alfa in juvenile-adult glycogenosis type 2 patients
作者:
Bruno Bembi
;
Sabrina Ravaglia
;
Federica Edith Pisa
;
Giovanni
Ciana
;
Agata Fiumara
;
Marco Confalonieri
;
Rossella Parini
;
Miriam Rigoldi
;
Arrigo Moglia
;
Alfredo Costa
;
Cesare Danesino
;
Maria Gabriela Pi
刊名:Molecular Genetics and Metabolism
出版年:2009
4.
36. Biochemical and molecular findings in a LIMP-2 deficient patient who presented with myoclonic epilepsy and no signs of renal involvement
作者:
Andrea Dardis
;
Mirella Filocamo
;
Serena Grossi
;
Giovanni
Ciana
;
Silvia Dominissini
;
Guido Rubboli
;
Maja Di Rocco
;
Bruno Bembi
刊名:Molecular Genetics and Metabolism
出版年:2009
5.
Cancer modeling: Modern imaging applications in the generation of novel animal model systems to study cancer progression and therapy
作者:
Alessia Stell
;
Andrea Biserni
;
Sara Della Torre
;
Gianpaolo R
o ;
Balaji Ramach
;
ran
;
Luisa Ottobrini
;
Giovanni
Lucignani
;
Adriana Maggi
;
Paolo
Ciana
关键词:
Tumor imaging
;
Pre-clinical models
;
Reporter mice
刊名:The International Journal of Biochemistry and Cell Biology
出版年:2007
6.
Techniques: Reporter mice – a new way to look at drug action
作者:
Maggi
;
Adriana
;
Ottobrini
;
Luisa
;
Biserni
;
Andrea
;
Lucignani
;
Giovanni
;
Ciana
;
Paolo
刊名:Trends in Pharmacological Sciences
出版年:2004
1
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