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CNKI期刊论文0611(36)
在“
Elsevier电子期刊
”中,
命中:
2,965
条,耗时:0.0559743 秒
在所有数据库中总计命中:
66,037
条
1.
Liver-based expression of the human alpha-
g
alactosidase A
g
ene (GLA) in a murine Fabry model results in continuous supra-physiolo
g
ical enzyme activity and effective substrate reduction
作者:
Marshall W. Huston
a
;
Maki
ko Yasuda
b
;
Silvere Pa
g
ant
b
;
Susan St. Martin
a
;
Scott Sproul
a
;
Yolanda Santia
g
o
a
;
Russel DeKelver
a
;
Michael C. Holmes
a
;
Robert
Desnick
b
;
Thomas Wechsler
a
刊名:Molecular
G
enetics and Metabolism
出版年:2017
2.
Acute Intermittent Porphyria in children: A case report and review of the literature
作者:
Manisha Balwani
;
MD
;
MS
a
;
1
;
Preeti Sin
g
h
;
MD
b
;
1
;
Anju Seth
;
MD
b
;
Ekta Malik Debnath
;
MD
c
;
Hetanshi Naik
;
MS
a
;
Dana Doheny
;
MS
;
C
G
C
a
;
Brenden Chen
;
MD
;
PhD
a
;
Maki
ko Yasuda
;
MD
;
PhD
a
;
Robert
J. Desnick
;
PhD
;
MD
a
;
robert
.desnick@mssm.edu
关键词:
ALAS1
;
Aminolevulinic acid synthase 1
;
HMBS
;
Hydroxymethylbilane synthase
;
ADP
;
Aminolevulinic acid dehydratase deficiency porphyria
;
PB
G
;
Porphobilino
g
en
;
ALA
;
Aminolevulinic acid
刊名:Molecular
G
enetics and Metabolism
出版年:2016
3.
G
ender differences in side effects and attitudes re
g
ardin
g
statin use in the Understandin
g
Statin Use in America and Gaps in Patient Education (USAGE) study
作者:
Dean
G
. Karalis
;
MD
;
FACC
;
FAHA
;
FNLA
a
;
dean.karalis@uphs.upenn.edu" class="auth_mail" title="E-mail the correspondin
g
author
;
Robert
A. Wild
;
MD
;
MPH
;
PhD
;
FNLA
b
;
Kevin C.
Maki
;
PhD
;
FNLA
;
FTOC
;
FACN
c
;
Ray
G
askins
;
MD
d
;
Terry A. Jacobson
;
MD
;
FAHA
;
FACP
;
FNLA
e
;
Crai
g
A. Sponseller
;
MD
f
;
Jerome D. Cohen
;
MD
;
FACC
;
FAHA
;
FNLA
g
关键词:
G
ender
;
Statins
;
Statin intolerance
;
Muscle pains
;
Myopathy
;
Compliance
刊名:Journal of Clinical Lipidolo
g
y
出版年:2016
4.
A mutant β-
g
lucosidase increases the rate of the cellulose enzymatic hydrolysis
作者:
Fá
;
bio K. Ta
maki
1
;
2
;
É
;
verton M. Araujo
1
;
Robert
o Rozenber
g
1
;
Sandro R. Marana
;
srmarana@iq.usp.br" class="auth_mail" title="E-mail the correspondin
g
author
关键词:
Sfβ
g
ly
;
β-
g
lucosidase GH1 from the fall armyworm Spodoptera fru
g
iperda
;
TrCel7A
;
cellobiohydrolase I from T. reesei
;
NPβfuc
;
p-nitrophenyl β-fucoside
;
NPβ
g
al
;
p-nitrophenyl β-
g
alactoside
;
NPβ
g
lc
;
p-nitrophenyl β-
g
lucoside
刊名:Biochemistry and Biophysics Reports
出版年:2016
5.
A velocity decomposition formulation for 2D steady incompressible liftin
g
problems
作者:
William J. Rosemur
g
y
;
Robert
F. Beck
;
Kevin J.
Maki
;
kj
maki
@umich.edu" class="auth_mail" title="E-mail the correspondin
g
author
关键词:
Incompressible Navier&ndash
;
Stokes flow
;
Velocity decomposition
;
Viscous potential flow
;
Viscous&ndash
;
inviscid interaction
刊名:European Journal of Mechanics - B/Fluids
出版年:2016
6.
Mono
g
enic and poly
g
enic determinants of sarcoma risk: an international
g
enetic study
作者:
Mandy L Ballin
g
er
;
PhD
a
;
c
;
f
;
*
;
David L
G
oode
;
PhD
c
;
f
;
*
;
Prof Isabelle Ray-Coquard
;
MD
i
;
Paul A James
;
MBChB
c
;
d
;
g
;
G
illian Mitchell
;
PhD
c
;
g
;
Eveline Niedermayr
;
BSc
c
;
f
;
Prof Ajay Puri
;
MS
j
;
Prof Joshua D Schiffman
;
MD
k
;
G
illian S Dite
;
PhD
e
;
Arcadi Cipponi
;
PhD
a
;
Prof
Robert
G
Maki
;
MD
m
;
Andrew S Brohl
;
MD
n
;
Prof Ola Myklebost
;
DPhil
o
;
p
;
Eva W Stratford
;
PhD
o
;
p
;
Susanne Lorenz
;
PhD
o
;
p
;
Sun
g
-Min Ahn
;
MD
q
;
Jin-Hee Ahn
;
MD
r
;
Jeon
g
Eun Kim
;
MD
r
;
Sue Shanley
;
MD
c
;
g
;
Victoria Beshay
;
PhD
h
;
Prof
Robert
Lor Randall
;
MD
l
;
Prof Ian Judson
;
MD
s
;
Beatrice Seddon
;
PhD
t
;
Prof Ian
G
Campbell
;
PhD
c
;
d
;
f
;
Mary-Anne Youn
g
;
MSc
c
;
g
;
Prof Rajiv Sarin
;
FRCR
u
;
Prof Jean-Yves Blay
;
MD
i
;
Seá
;
n I O'Dono
g
hue
;
PhD
b
;
v
;
Prof David M Thomas
;
FRACP
a
;
d.thomas@
g
arvan.or
g
.au" class="auth_mail" title="E-mail the correspondin
g
author
;
for the International Sarcoma Kindred Study
&da
gg
er
;
刊名:The Lancet Oncolo
g
y
出版年:2016
7.
Pro
g
ranulin Deficiency Promotes Circuit-Specific Synaptic Prunin
g
by Micro
g
lia via Complement Activation
作者:
Hansen Lui
1
;
18
;
Jiashen
g
Zhan
g
1
;
Stefanie R.
Maki
nson
2
;
Michelle K. Cahill
1
;
Kevin W. Kelley
3
;
Hsin-Yi Huan
g
1
;
19
;
Yulei Shan
g
1
;
Michael C. Oldham
4
;
Lauren Herl Martens
5
;
Fuyin
g
Gao
6
;
G
iovanni Coppola
6
;
Steven A. Sloan
7
;
Christine L. Hsieh
8
;
Charles C. Kim
9
;
20
;
Eileen H. Bi
g
io
10
;
Sandra Weintraub
10
;
Marek-Marsel Mesulam
10
;
Rosa Rademakers
11
;
Ian R. Mackenzie
12
;
William W. Seeley
13
;
Anna Karydas
13
;
Bruce L. Miller
13
;
Barbara Borroni
14
;
Robert
a
G
hidoni
15
;
Robert
V. Farese Jr.
16
;
Jeanne T. Paz
2
;
Ben A. Barres
7
;
Eric J. Huan
g
1
;
17
;
eric.huan
g
2@ucsf.edu" class="auth_mail" title="E-mail the correspondin
g
author
刊名:Cell
出版年:2016
8.
When do peers matter?: A cross-country perspective
作者:
Bill B. Francis
a
;
Iftekhar Hasan
b
;
c
;
G
er
g
ana L. Kostova
a
;
g
lkostova@
g
mail.com" class="auth_mail" title="E-mail the correspondin
g
author
关键词:
G
2
;
G
32
刊名:Journal of International Money and Finance
出版年:2016
9.
Community-wide Interventions to Prevent Skin Cancer: Two Community
G
uide Systematic Reviews
作者:
Paramjit K. Sandhu
;
MD
;
MPH
1
;
psandhu@cdc.
g
ov" class="auth_mail" title="E-mail the correspondin
g
author
;
Randy Elder
;
PhD
1
;
Mona Patel
;
MPH
1
;
Mona Saraiya
;
MD
;
MPH
2
;
Dawn M. Holman
;
MPH
2
;
Frank Perna
;
EdD
;
PhD
3
;
Robert
A. Smith
;
PhD
4
;
David Buller
;
PhD
5
;
Crai
g
Sinclair
;
BEd
;
MPPM
6
;
Anthony Reeder
;
BA
;
PhD
7
;
Jennifer
Maki
n
;
MSc
8
;
Bronwen McNoe
;
MPH
7
;
Karen
G
lanz
;
PhD
;
MPH
9
;
the Community Preventive Services Task Force
刊名:American Journal of Preventive Medicine
出版年:2016
10.
Innovative nursin
g
care models and culture of health: Early evidence
作者:
G
rant R. Martsolf
;
PhD
;
MPH
;
RN
a
;
martsolf@rand.or
g
" class="auth_mail" title="E-mail the correspondin
g
author
;
Tamika
G
ordon
;
MS
a
;
b
;
Linnea Warren May
;
MPH
a
;
Diana Mason
;
PhD
;
RN
;
FAAN
c
;
d
;
Cheryl Sullivan
;
MSES
d
;
Antonia Villarruel
;
PhD
;
FAAN
e
关键词:
Nursin
g
;
Culture of health
刊名:Nursin
g
Outlook
出版年:2016
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