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内部出版物
在“
SpringerLink电子期刊
”中,
命中:
112
条,耗时:小于0.01 秒
1.
Validation of the Italian version of the
SBMA
Functional Rating Scale as outcome measure
作者:
Giorgia Querin
;
Elisa DaRe
;
Ilaria Martinelli
;
Luca Bello…
关键词:
SBMA
;
Functional scale
;
Biomarkers
;
Italian version
;
Validation
刊名:Neurological Sciences
出版年:2016
2.
The Role of the Protein Quality Control System in
SBMA
作者:
Paola Rusmini
;
Valeria Crippa
;
Riccardo Cristofani…
关键词:
Androgen receptor
;
Polyglutamine
;
CAG triplet repeat
;
Neurodegeneration
;
Motoneuron diseases
;
Muscle
;
SBMA
;
Testosterone
;
Autophagy
;
Protein quality control system
;
Proteotoxicity
;
Proteasome
;
UPR
;
ERAD
;
HSPB8
;
Chaperones
;
Misfolded protein
;
Aggregation
;
BAG3
;
Rusmini Paola
;
Crippa Valeria
;
Greensmith Linda
;
and Poletti Angelo equally contributed to this study.
刊名:Journal of Molecular Neuroscience
出版年:2016
3.
Targeted Molecular Therapies for
SBMA
作者:
Carlo Rinaldi
;
Bilal Malik
;
Linda Greensmith
关键词:
Spinal and bulbar muscular atrophy
;
Drug target
;
Neuromuscular disease
;
Molecular pathogenesis
刊名:Journal of Molecular Neuroscience
出版年:2016
4.
Glycolytic-to-oxidative fiber-type switch and mTOR signaling activation are early-onset features of
SBMA
muscle modified by high-fat diet
作者:
Anna Rocchi
;
Carmelo Milioto
;
Sara Parodi
;
Andrea Armirotti…
刊名:Acta Neuropathologica
出版年:2016
5.
Exercise Therapy in Spinobulbar Muscular Atrophy and Other Neuromuscular Disorders
作者:
Julia Rebecka Dahlqvist
;
John Vissing
关键词:
Spinobulbar muscular atrophy
;
SBMA
;
Kennedy disease
;
Exercise
刊名:Journal of Molecular Neuroscience
出版年:2016
6.
Hypospadias as a novel feature in spinal bulbar muscle atrophy
作者:
Anna Skarin Nordenvall
;
Martin Paucar
;
Catarina Almqvist…
关键词:
Spinal bulbar muscle atrophy
;
CAG expansion
;
Androgen receptor
;
Hypospadias
刊名:Journal of Neurology
出版年:2016
7.
In Vitro and In Vivo Modeling of Spinal and Bulbar Muscular Atrophy
作者:
Maria Pennuto
;
Manuela Basso
关键词:
Spinal and bulbar muscular atrophy
;
Androgen receptor
;
Cell models
;
Neuronal cells
;
Muscle cells
;
Mouse models
;
Transgenic mice
;
Knock
;
in mice
刊名:Journal of Molecular Neuroscience
出版年:2016
8.
Inhibition of the Androgen Receptor by Antiandrogens in Spinobulbar Muscle Atrophy
作者:
Aria Baniahmad
关键词:
Kennedy’s Disease
;
Polyglutamine expansion syndrome
;
Neurotoxicity
刊名:Journal of Molecular Neuroscience
出版年:2016
9.
Onset Manifestations of Spinal and Bulbar Muscular Atrophy (Kennedy's Disease)
作者:
Josef Finsterer
;
Gianni Soraru
关键词:
Spinal and bulbar muscular atrophy
;
Early symptoms
;
Initial manifestations
;
Kennedy’s disease
;
Bulbar functions
;
CAG
;
repeats
;
Poly
Q ;
Bulbospinal neuronopathy
;
Spinobulbar muscular atrophy
;
Motor neuron disease
刊名:Journal of Molecular Neuroscience
出版年:2016
10.
Polyglutamine androgen receptor-mediated neuromuscular disease
作者:
Elisa Giorgetti
;
Andrew P. Lieberman
关键词:
Spinal and bulbar muscular atrophy
;
CAG/polyglutamine disorder
;
Androgen receptor
;
Skeletal muscle
;
Motor neuron
刊名:Cellular and Molecular Life Sciences (CMLS)
出版年:2016
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