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条
1.
Mutations in ATP6
V
1E1 or ATP6V1A
C
ause Autosomal-Re
c
essi
v
e Cutis Laxa
作者:
Tim
V
an Damme
1
;
25
;
Thatjana Gardeit
c
hik
2
;
3
;
25
;
Miski Mohamed
2
;
25
;
Sergio Guerrero-
C
astillo
4
;
5
;
26
;
Peter Freisinger
6
;
26
;
Bre
c
ht Guillemyn
1
;
26
;
Ariana Kariminejad
7
;
26
;
Daisy Dalloyaux
2
;
5
;
Sanne
v
an Kraaij
2
;
5
;
Dirk J. Lefeber
5
;
8
;
Delfien Syx
1
;
Wouter Steyaert
1
;
Riet De Ry
c
ke
9
;
10
;
Alexander Hois
c
hen
3
;
Erik-Jan Kamsteeg
3
;
Sunnie Y. Wong
11
;
Monique
v
an S
c
herpenzeel
5
;
8
;
Payman Jamali
12
;
Ulri
c
h Brandt
4
;
5
;
Leo Nijtmans
4
;
5
;
G.
C
hristoph Korenke
13
;
Brian H.Y.
C
hung
14
;
C
hristopher C.Y. Mak
14
;
Ingrid Hausser
15
;
Uwe Kornak
16
;
17
;
Bjö
;
rn Fis
c
her-Zirnsak
16
;
17
;
Tim M. Strom
18
;
Thomas Meitinger
18
;
Yasemin Alanay
19
;
Gulen E. Utine
20
;
Peter K.
C
. Leung
14
;
Sia
v
ash Ghaderi-Sohi
7
;
Paul
C
ou
c
ke
1
;
Sofie Symoens
1
;
Anne De Paepe
1
;
C
hristian Thiel
21
;
Tobias B. Haa
c
k
18
;
22
;
23
;
Fransiska Malfait
1
;
27
;
E
v
a Mora
v
a
11
;
24
;
27
;
Bert
C
allewaert
1
;
27
;
bert.
c
allewaert@ugent.be
;
Ron A. We
v
ers
5
;
27
;
ron.we
v
ers@radboudum
c
.nl
关键词:
V
-ATPase
;
ATP6
V
1E1
;
ATP6
V
1A
;
c
utis laxa
;
autosomal re
c
essi
v
e
;
AR
C
L2
;
c
ongenital disorder of gly
c
osylation
;
C
DG
;
Golgi apparatus
;
c
ellular traffi
c
king
刊名:The Ameri
c
an Journal of Human Geneti
c
s
出版年:2017
2.
C
omparing the lumines
c
en
c
e pro
c
esses of Y
V
O
4
:Eu and
c
ore-shell YVO
4
@YF
3
nano
c
rystals with bulk-YVO
4
:Eu
作者:
L. Shirmane
a
;
liana.shirmane@gmail.
c
om"
c
lass="auth_mail" title="E-mail the
c
orresponding author
;
C
. Feldmann
b
;
V
. Pankrato
v
a
;
c
;
d
;
v
ladimirs.pankrato
v
s@oulu.fi"
c
lass="auth_mail" title="E-mail the
c
orresponding author
;
v
pank@latnet.l
v
"
c
lass="auth_mail" title="E-mail the
c
orresponding author
;
v
ladimirs.pankrato
v
s@maxi
v
.se"
c
lass="auth_mail" title="E-mail the
c
orresponding author
关键词:
Y
V
O4
;
Eu3+
;
Nanophosphors
;
C
ore-Shelled nanoparti
c
les
;
Lumines
c
en
c
e
;
Syn
c
hrotron radiation
刊名:Physi
c
a B: Physi
c
s of Condensed Matter
出版年:2017
3.
A
c
ommer
c
ial por
c
ine
c
ir
c
o
v
irus (PCV) type 2a-based
v
a
cc
ine redu
c
es PCV2d
v
iremia and shedding and pre
v
ents PCV2d transmission to naï
v
e pigs under experimental
c
onditions
作者:
Tanja Opriessnig
a
;
b
;
Tanja.Opriessnig@roslin.ed.a
c
.uk
;
C
hao-Ting Xiao
b
;
c
;
Patri
c
k G. Halbur
b
;
Pris
c
illa F. Gerber
a
;
Shannon R. Matzinger
d
;
Xiang-Jin Meng
d
关键词:
Por
c
ine
c
ir
c
o
v
irus
;
P
CV
2
;
P
CV
2d
;
V
a
cc
ination
;
V
a
cc
ine effi
c
a
c
y
;
Transmission
刊名:
V
a
cc
ine
出版年:2017
4.
Bone tissue response indu
c
ed by bioa
c
ti
v
e polymer fun
c
tionalized Ti6Al4V surfa
c
es: In
v
itro and in
v
i
v
o study
作者:
Helena P. Felgueiras
a
;
felgueiras.helena@gmail.
c
om
;
Adeline De
c
ambron
b
;
c
;
Mathieu Manassero
b
;
c
;
Louise Tulasne
c
;
Margaret D.M. E
v
ans
d
;
V
&ea
c
ute
;
ronique
V
iateau
b
;
c
;
V
&ea
c
ute
;
ronique Migonney
a
关键词:
Ti6Al4
V
;
Poly(sodium styrene sulfonate) grafting
;
C
ollagen type I
;
Bone morphogeneti
c
protein-2
;
Osteogenesis
;
Osseointegration
刊名:Journal of
C
olloid and Interfa
c
e S
c
ien
c
e
出版年:2017
5.
C
hara
c
terization of
c
ulture filtrate proteins R
v
1197 and R
v
1198 of ESAT-6 family from My
c
oba
c
terium tuber
c
ulosis H37R
v
作者:
Himanshu Pandey
a
;
Sarita Tripathi
a
;
Kan
c
han Sri
v
asta
v
a
c
;
Dinesh K. Tripathi
b
;
Mrigank Sri
v
asta
v
a
d
;
Surya Kant
c
;
Kishore K. Sri
v
asta
v
a
b
;
kishore@
c
dri.res.in
;
Ashish Arora
a
;
ashish_arora@
c
dri.res.in
关键词:
My
c
oba
c
terium tuber
c
ulosis
;
ESAT-6 family
;
R
v
1197
;
R
v
1198
;
Serorea
c
ti
v
ity
;
V
a
cc
ine
刊名:Bio
c
himi
c
a et Biophysi
c
a A
c
ta (BBA) - General Subje
c
ts
出版年:2017
6.
Semi
c
ondu
c
ting properties of
c
old sintered
V
2
O
5
c
erami
c
s and Co-sintered V
2
O
5
-PEDOT:PSS
c
omposites
作者:
Jing Guo
a
;
jug34@psu.edu
;
Hanzheng Guo
a
;
Damoon Sohrabi Baba Heidary
a
;
Shui
c
hi Funahashi
a
;
b
;
C
li
v
e A. Randall
a
;
c
ar4@psu.edu
关键词:
C
old sintering pro
c
ess
;
Oxide semi
c
ondu
c
tor
;
V
2O5
;
V
2O5-PEDOT
;
PSS
c
omposite
;
Metal-insulator transition
刊名:Journal of the European
C
erami
c
So
c
iety
出版年:2017
7.
V
γ1
+
γδT, early
c
ardia
c
infiltrated innate population dominantly produ
c
ing IL-4, prote
c
t mi
c
e against CVB3 myo
c
arditis by modulating IFNγ
+
T response
作者:
Fangfang Wan
1
;
Kepeng Yan
1
;
Dan Xu
;
Qian Qian
;
Hui Liu
;
Min Li
;
Wei Xu
;
xuweifd828@126.
c
om
关键词:
V
iral myo
c
arditis
;
CV
B3
;
γδT
;
V
γ1
;
IL-4
刊名:Mole
c
ular Immunology
出版年:2017
8.
LiMnPO
4
·Li
3
V
2
(PO
4
)
3
c
omposite
c
athode material deri
v
ed from Mn(VO
3
)
2
nanosheet pre
c
ursor
作者:
Zhihong Lei
a
;
Jun Yang
a
;
Yang He
b
;
Yuyan Shao
c
;
S
c
ott X. Mao
b
;
C
hongming Wang
c
;
Yanna Nuli
a
;
Jiulin Wang
a
;
wangjiulin@sjtu.edu.
c
n
关键词:
LiMnPO4
;
Li3
V
2(PO4)3
;
Mn(
V
O3)2
;
C
athode material
;
Lithium ion battery
刊名:Journal of Alloys and
C
ompounds
出版年:2017
9.
Ele
c
tropolishing and ele
c
tropolishing-related allowan
c
es for powder bed sele
c
ti
v
ely laser-melted Ti-6Al-4V alloy
c
omponents
作者:
V
. Urlea
;
V
. Brailo
v
ski
;
v
.brailo
v
@gmail.
c
om
;
v
ladimir.brailo
v
ski@etsmtl.
c
a
关键词:
Additi
v
e manufa
c
turing
;
Sele
c
ti
v
e laser melting
;
Build orientation
;
Surfa
c
e finish
;
Ele
c
tropolishing allowan
c
es
;
Ti-6Al-4
V
刊名:Journal of Materials Pro
c
essing Te
c
hnology
出版年:2017
10.
U
V
-B Per
c
ei
v
ed by the UVR8 Photore
c
eptor Inhibits Plant Thermomorphogenesis
作者:
S
c
ott Hayes
1
;
2
;
6
;
Ashutosh Sharma
1
;
6
;
Donald P. Fraser
1
;
Martine Tre
v
isan
3
;
C
. Kester Cragg-Barber
1
;
Eleni Ta
v
ridou
4
;
C
hristian Fankhauser
3
;
Gareth I. Jenkins
5
;
Keara A. Franklin
1
;
7
;
kerry.franklin@bristol.a
c
.uk
关键词:
U
V
-B
;
Arabidopsis
;
U
V
R8
;
high temperature
;
auxin
;
hypo
c
otyl
;
HFR1
;
PIF4
刊名:
C
urrent Biology
出版年:2017
1
2
3
4
5
6
7
8
9
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